“…Angiosarcoma is a rare disease, and thus, there is currently no standard treatment plan, particularly not for PPA. Patients with pulmonary angiosarcoma have been treated with surgical resection ( 5 , 11 , 17 , 22 ), adjuvant radiotherapy ( 8 , 20 , 22 ), chemotherapy ( 20 , 26 ), immunotherapy ( 27 , 28 ) and combined therapy ( 10 , 16 , 20 ). It has been proposed that surgery was the most effective treatment, which should be considered as early as possible for resectable tumors ( 5 , 17 ).…”