Functioning left uterine horn with cervico-vaginal atresia and ovarian maldescent – an unclassified Müllerian anomaly treated with horn-vaginal anastomosis

Bagga, Rashmi; Muthyala, Tanuja; Saha, Pradeep Kumar; Kalra, Jaswinder; Singla, Rimpi; Arora, Aashima; Singh, Tulika

doi:10.1080/01443615.2018.1430127

Cited by 4 publications

(5 citation statements)

References 11 publications

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“…However, although the ovarian embryological development follows a different path than the uterus and fallopian tubes, the UO incidence is higher in the presence of uterine anomalies, particularly the unicornuate uterus (UU) caused by a lack of development of one Müllerian duct or by a disturbed descent to its proper location. 36,37 This fact supports the theory of a multifactorial polygenic process at the end of the second gestational month. 8,11,14 Some claim that the abnormal ovarian migration could affect the paramesonefrotic fusion, 4,32 while others hypothesize that the descent of the ovary depends on a proper development of the Müllerian system.…”

Section: Pathogenesis and Associated Malformationssupporting

confidence: 82%

Diagnostic and Management of Undescended Ovary – A Preoperative Dilemma: A Case-Based Systematic Review

Ștefanopol¹,

Baroiu²,

Constantin³

et al. 2022

IJWH

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Undescended ovary (UO) is an uncommon congenital condition characterized by the presence of the adnexa above the common iliac vessels, with an estimated incidence of 0.3-2%. Because of its rarity, it is usually presented as a case report. A thorough knowledge of the ovarian embryological development is essential for the clinician, who must be warned about the possibility of associated Müllerian and renal malformations. There may be asymptomatic patients, incidentally diagnosed during infertility evaluation, but when symptoms occur, these are unspecific and most often this disorder is misdiagnosed, the accurate diagnosis being established intraoperatory. The malignant potential of an UO is accepted, although no such cases were reported. The role of the UO in infertility is still unclear, despite evidence of its normal function. Complications are linked to the ovary (cyst formation, cyst ruptures or tumors) or to the undescended fallopian tube (ectopic pregnancies). The management should be conservative, but there is no consensus about whether it is necessary to excise the ipsilateral undescended tube. We included a short case presentation of an UO cystadenoma misdiagnosed as a renal cyst, which depicts all diagnostic and management dilemmas and inspired us to write this review. The present literature review includes all the cases reported from the early 20th century to the present, with updated data about epidemiology, pathophysiology, clinical and imaging diagnosis, treatment options and prognosis of this rare condition. This paper aims to establish some directions in the diagnosis and management of similar patients and to remind us that, no matter how advanced the imaging investigation techniques might be, a correct preoperative diagnosis may often be missed.

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Section: Pathogenesis and Associated Malformationssupporting

confidence: 82%

Diagnostic and Management of Undescended Ovary – A Preoperative Dilemma: A Case-Based Systematic Review

Ștefanopol¹,

Baroiu²,

Constantin³

et al. 2022

IJWH

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“…Cervicovaginal agenesis is a rare congenital anomaly of the female genital tract. Only few scattered cases and case series are reported in the literature[ 4 5 6 7 8 9 10 11 12 13 14 15 16 17 18 ] [ Table 1 ].…”

Section: Discussionmentioning

confidence: 99%

“…On the contrary, as surgical skills and assisted reproductive technique are evolving over the time, conservative surgery could be considered as the first-line treatment. [ 9 10 11 12 14 16 17 18 ] Patient's femininity and a distortion of her physical image which can affect her self-esteem should be kept in mind. In our case, we preferred conservative surgery over hysterectomy with due consent from the patient and her parents.…”

Section: Discussionmentioning

confidence: 99%

The Path of Birth is Not Always Normal

Khoiwal

Singh

Agarwal

et al. 2021

Gynecology and Minimally Invasive Therapy

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Cervical agenesis is a rare congenital Mullerian anomaly. Its association with vaginal agenesis is further rare, reported in 39% of cases of cervical agenesis. The conventional treatment for this condition was hysterectomy. However, with evolving surgical skills and assisted reproductive techniques, conservative surgery could be considered as the first-line treatment in the current era. We report one such case of cervicovaginal agenesis in a 13-year-old adolescent girl managed successfully with cervicovaginoplasty. The patient was relieved of cyclical pain abdomen and resumed menstrual cycles postoperatively.

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“…Поверхня нирки у новонарождених і дітей раннього віку горбиста за рахунок часточкової будови нирки. Бугристість нирки зберігається до 2-5 років, а потім поступово зникає [6]. У дітей раннього віку товщина мозкового шару нирки переважає над товщиною коркового шару (4:1).…”

Section: результати обговоренняunclassified

Modern view on the germ and embryogenesis of the urinary organs

Bulyk¹,

Popeliuk²,

Melnyk³

et al. 2022

Rep. of Vinnytsia Nation. Med. Univ.

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Annotation. The literature is devoted to the analysis of scientific literature for the last 10 years from the electronic databases "PubMed" and "National Library of Ukraine named after V. I. Vernadsky", which are devoted to the study of the formation and development of organs and structures of the urinary system. The consequences of perinatal morphogenesis play the most essential role in the causes and contribution to many congenital malformations (CM), stillbirths, and infant morbidity. According to the Medical and Genetic Service of the Ministry of Health of Ukraine, up to 3,000 cases of CM of various organs and systems are recorded annually among newborns in Ukraine. CM of the genitourinary system ranks 3rd in frequency, among which CM of the female genitalia is up to 6 %. These figures are somewhat subjective, as a certain percentage of pathology of the female reproductive system is detected only when a girl reaches childbearing age, which greatly complicates the choice of methods and effectiveness of treatment. The rapid development of the genitourinary system of the fetus requires morphologists to comprehensively study the patterns of morphogenesis and the development of topographic and anatomical relationships of the reproductive system and urinary tract in the early period of human ontogenesis. The problem of combining information about the structural organization of the urinary tract and genital system into a consolidated morphofunctional unit is one of the cardinal problems of perinatal urology. The final formation of the urogenital organs is as follows. The initial kidneys' replacement with the permanent ones, metanephros, begins to form, from the same nephrogenic cord that gave rise to the primary kidney. The proper permanent renal parenchyma develops from the nephrogenic cord (renal tubuli). From the 3rd month, the permanent kidneys replace the mesonephros as the excretory organs already function. Thus, the embryonic development of the genitals is closely related to the development of the urinary tract and kidneys. Therefore, the CM of these two systems often occurs together. Active introduction of perinatal prophylaxis of urogenital organs requires modern approaches and methods of examination of intrauterine life. Therefore, the complex of embryotopographic studies attains special significance, having combined the consideration of organically critical periods of development with the understanding of the peculiarities of the spatial relationships of organs and structures of the genitourinary system.

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Functioning left uterine horn with cervico-vaginal atresia and ovarian maldescent – an unclassified Müllerian anomaly treated with horn-vaginal anastomosis

Cited by 4 publications

References 11 publications

Diagnostic and Management of Undescended Ovary – A Preoperative Dilemma: A Case-Based Systematic Review

Diagnostic and Management of Undescended Ovary – A Preoperative Dilemma: A Case-Based Systematic Review

The Path of Birth is Not Always Normal

Modern view on the germ and embryogenesis of the urinary organs

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