“…The small intestine and large intestine are the next most frequently affected organs, in that order [ 2 ]. A novel concept on extranodal malignant lymphomas resulting from MALT in the GI tract, salivary gland, lung, and thyroid was presented by Isaacson and Wright in 1983 [ 2 , [10] , [11] , [12] ]. Only 5 appendiceal MALTomas have, as far as we are aware, been documented in the literature.…”