“…The etiology of DCLV is obscure, but literature suggests endocardial fibroelastosis and cardiomyopathy as presumed etiology 2,3 . Iorgoveanu et al 4 stated that defective RAC1 gene results in impaired elongation and cytoskeleton organization in cardiomyocytes, thus resulting in DCLV. It results from an anomalous septum or muscle bundle which divides the left ventricular cavity into two chambers, named as the main left ventricular chamber (MLVC) and accessory chamber (AC) 2,3,5 .…”