Hirayama Disease

Abstract

Hirayama disease (HD) is a rare benign lower motor neuron disorder in the young with a male preponderance and usually affecting one upper extremity. It is characterized by the insidious onset and progressive weakness and wasting of a distal extremity. Generally, this disease is considered as a benign and nonprogressive motor neuron disease that stabilizes within five years of onset. We describe a 20-year-old male patient who experienced left distal upper extremity amyotrophy with no sensorial abnormality.