Hirschsprung Diseases should be Treated by Single or Two Stage Operations? A Case Report in a Resource-Low Setting in Cameroon

Abstract

Background: Hirschsprung disease is a developmental disorder characterized by the absence of ganglia in the distal colon, resulting in a functional obstruction. Hirsch sprung disease is common in the paediatric age group (neonatal period). They represent worldwide 1/1500-1/7000 newborn. The male: female ratio is 4:1. Case Report: We report the case of Hirsch sprung diseases diagnosed in a one month old neonate who presented with abdominal distension and recurrent constipation since birth. The past history was relevant for delay emission of meconium. A rectosigmoid contrast enema transition zone was observed and a diagnosis of hirschsprung disease was made. The patient was treated through asingle stage operation, trans-anal pull throughin YGOPH. Conclusion: Accurate reporting and creation of registry and data bases are important measures to curb the mortality and morbidity associated with this paediatric surgical condition