IgG4-related Disease: A Concise Review of the Current Literature

Retroperitoneal fibrosis associated with orbital pseudotumor without evidence of IgG4: A case report with review of literature

“…Up to 50% of patients with IgG4-RD usually have a history of chronic allergic conditions. It can affect virtually any territory and the territories most frequently affected are pancreas, salivary glands and lymph nodes (5). The diagnosis of this entity is based on clinical, serologic and pathological studies.…”

“…characterized by the infiltration of IgG4-positive plasma cells in the affected tissues (mostly pancreas, salivary glands and lymph nodes, although it can affect a large number of tissues) (3,5,6). We present the case of a 59-year-old woman diagnosed with retroperitoneal fibrosis.…”

Sclerosing angiomatoid nodular transformation of the spleen presenting rapid growth after adrenalectomy: Report of a case

“…In our case, EBV was not detected by EBER, and although we did not measure serum IgG4 levels, immunochemical staining for IgG4 yielded positive results, supporting the possibility that SANT was related to IgG4-associated disease. IgG4-associated disease is the term used to refer to a condition characterized by lymphoplasmacytic infiltration, fibrosis and increased numbers of IgG4+ cells present in tissue [16]. This disease has an allergic background and is immune-mediated.…”

A Case of Type 1 Autoimmune Pancreatitis (AIP), a Form of IgG4-Related Disease (IgG4-RD)

“…The diagnosis of IgG4-RD is made between the ages of 50 years and 70 years, but IgG4-RD has also been diagnosed in children [ 10 ]. IgG4-RD can involve any tissue but it frequently affects the pancreas, salivary glands, and lymph nodes [ 11 , 12 ]. Other common extra-pancreatic manifestations are tubulointerstitial nephritis, dacryoadenitis, and periaortitis [ 13 ].…”