IgG4-Related Sclerosing Disease

Abstract

A t s u t a k e O k a m o t o , D e p a r t m e n t o f S u rg e r y, Tokyo Metropolitan Komagome Hospital, Tokyo 113-8677, Japan Kamisawa T et al . IgG4-related sclerosing disease 3949has been observed in various extrapancreatic lesions [9] . Furthermore, many IgG4-related sclerosing diseases of organs other than the pancreas have been recently reported. Although the nomenclature differs, IgG4related sclerosing disease has been noted in hepatology, cholangiology, rheumatology, urology, nephrology, respirology, endocrinology, pathology, and radiology, as well as pancreatology. Based on our experience with 50 AIP patients, this review focuses on the clinical, laboratory, imaging, and histopathological features of IgG4-related sclerosing disease, including AIP. 3954