Interrupted inferior vena cava and partial anomalous pulmonary venous return with atrial septal defect in a 38-year-old adult: a case report

Abstract

We present a woman having congenital anomalies of the inferior vena cava and partial anomalous pulmonary venous return from the right lung with atrial septal defect in a 38-year-old. Congenital anomalies of inferior vena cava are rare. They are seen more often in young males. If there are not other anomalies, they are latent for a long time. Peripheral venous thrombosis, chronic venous insufficiency, dyspnea and fatigue are often the first symptoms of these anomalies. Surgical repair of atrial septal defect with partial anomalous pulmonary venous return include provision of durably unobstructed systemic and pulmonary venous pathways, closure of the atrial septal defect, and avoidance of arrhythmias. The diagnosis has been determined by compression ultrasonography with color doppler assessment, multidetector computed tomography angiography and echocardiography.

Prenatal diagnosis of isolated interrupted inferior vena cava with azygos continuation to superior vena cava

“…[4] Symptoms and prognosis are related to associated congenital heart disease. [23] This finding also can have an impact on interventional procedures (IVC filter placement) and surgical procedures (esophagectomy, liver transplants). According to Sheley and colleagues,[12] post-natal survival was related to the severity of the associated heart disease.…”

“…Most of the previous reports of isolated IVC interruption have been in adults. [ 2 8 13 ] We feel the bi-caval view is extremely useful in demonstrating this anomaly along with demonstration of the azygos continuation to the SVC. Pre-natal counseling for this vascular anomaly should include the likelihood of possible development of sick sinus syndrome in future and the increased risk for venous thrombosis.…”

“…[ 1 ] The incidence of this anomaly approximates 0.6% in patients with congenital heart defects including atrio-ventricular canal, anomalously connecting pulmonary veins, double outflow right ventricle, large atrial septal defect, pulmonary stenosis or atresia, and sick sinus syndrome. [ 2 3 ] This is often associated with visceral and cardiac malpositions typically associated with left isomerism. [ 4 5 ] The most common pattern is azygos continuation with normal position of the heart and abdominal viscera.…”

An unusual case of uninterrupted inferior vena cava with accessory hemizygous channel: An incidental finding in a child

“…The prevalence of azygos continuation of the IVC approaches 0.6–2% in association with congenital heart defects and less than 0.3% when isolated. [ 2 ]…”

Congenitally Corrected Transposition of the Great Arteries with Anomalous Inferior Vena Cava Drainage: Multimodality Imaging

“…We present a case of a woman diagnosed with CCTGA who, on echocardiography, had anomalous venous drainage where the inferior vena cava (IVC) bypassed the right atrium (RA) and drained into the azygos system. Interrupted IVC with azygos continuation is rare in adults, 1,2 and should be considered in complex congenital cardiac cases. In pediatric congenital heart disease cases, interrupted IVC with azygos continuation is more common, and it is important to exclude partial anomalous pulmonary venous return 3,4 .…”