Interventricular septum aneurysm: Two differently managed cases and association with bicuspid aortic valve

Deaconu, Alexandru; Iancovici, S; Wellnhofer, Ernst; Berger, Alexander; Gebker, Rolf; Pieske, Burkert; Pašić, Miralem; Kelle, Sebastian

doi:10.1016/j.ijcard.2015.08.039

Cited by 2 publications

(2 citation statements)

References 9 publications

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“…The combination of bicuspid valve and membranous interventricular septal aneurysm is extremely rare and few cases are reported in the literature. Deaconu et al described 2 cases of bicuspid valve and interventricular septal aneurysm [13]; both cases were similar to our patient in that the interventricular septal aneurysm was an incidental finding. One of the cases was a 18-year-old female with prior surgical correction of an aortic coarctation.…”

Section: Discussionsupporting

confidence: 87%

Management of Late-Presenting Congenital Combined Heart Defect – Bicuspid Aortic Valve and Ventricular Septal Aneurysm

2020

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Objective:Rare disease Background:Bicuspid aortic valve is the most common congenital heart malformation, encountered in 1-2% of the population, while interventricular septal defect and patent ductus arteriosus are the most common congenital malformations associated with bicuspid aortic valve. Although bicuspid valve can have no clinical manifestation, patients with bicuspid valve are prone to develop vascular abnormalities. Aortic dilatation is the most common of these abnormalities, which in turn can lead to serious complications and often requires surgical treatment. Coexistence of bicuspid aortic valve and interventricular septal aneurysm is very extremely rare. Case Report:We present a very rare case of a female patient with combined congenital cardiac pathology. The patient was asymptomatic until age 68 years, and presented with nonspecific persistent cough. The diagnostic work-up for the unexplained cough showed normal function of the bicuspid valve and an ascending aorta aneurysm accompanied with interventricular septal aneurysm. The patient was referred for surgery. The diagnostic workup and the decision for surgical treatment were thoroughly discussed to determine whether it was a true or a false aneurysm. Conclusions:The presented case is an example of late diagnosis of a congenital cardiac defect. The silent evolution and the scarce clinical presentation led to incidental discovery of the pathology, which was fully assessed only by computed tomography. Although echocardiography is essential for discovering heart defects, non-invasive imaging techniques are required for detailed morphological assessment and for planning optimal surgical treatment.

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Section: Discussionsupporting

confidence: 87%

Management of Late-Presenting Congenital Combined Heart Defect – Bicuspid Aortic Valve and Ventricular Septal Aneurysm

2020

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“…Therapeutic management is often problematic when VSA is incidentally diagnosed in asymptomatic patient, and when discovered on autopsy the dilemma is how can it explain an "unexplained" death. Natural course of this disease remains unpredictable; even if in some cases favorable outcomes are reported without any therapeutic intervention [6,7] serious and sometimes fatal complications may occurs [8,9]. Cardiac rhythm and conduction disorders in patient with VSA were described in several papers [10,11].…”

Section: Discussionmentioning

confidence: 99%

Interventricular Septal Aneurysm: an Exceptional cause of Sudden Death in Young Adult

Yomn¹

2018

JFSCI

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Interventricular septum aneurysm: Two differently managed cases and association with bicuspid aortic valve

Cited by 2 publications

References 9 publications

Management of Late-Presenting Congenital Combined Heart Defect – Bicuspid Aortic Valve and Ventricular Septal Aneurysm

Management of Late-Presenting Congenital Combined Heart Defect – Bicuspid Aortic Valve and Ventricular Septal Aneurysm

Interventricular Septal Aneurysm: an Exceptional cause of Sudden Death in Young Adult

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