Intestinal obstruction due to kaposiform hemangioendothelioma in a 1-month-old infant

Abstract

Rationale:Kaposiform hemangioendothelioma (KHE) is an aggressive vascular tumor, mainly occurring in infants and young children and previously reported cases were mainly cutaneous or visceral form. Intestinal kaposiform hemangioma was first reported in 2012. Intestinal type KHE showed better prognosis if the lesion was limited in the gastrointestinal tract and coagulopathy was not accompanied. Since the number of reported cases is small, further study for treatment options and prognosis need to be done.Patient concerns:We described the case of a 1-month-old female who had abdominal distention and bilious vomiting.Diagnoses:She was suspected as intestinal obstruction after diagnostic work up.Interventions:Surgical exploration was performed and jejunal obstruction with a mass was identified. Small bowel segmental resection and anastomosis was performed.Outcomes:The patient discharged with symptom free. Through the pathological examination, the mass was identified as intestinal type KHE.Lessons:Intestinal KHE can cause bowel obstruction and be managed successfully with complete surgical resection. More cases should be reported and further evaluation for treatment options and prognosis evaluation is necessary.

Kaposiform hemangioma of jejunum in a newborn: A case report and review of literature

“…Differential diagnoses include the duplication cyst, the mesentery cyst and the extrinsic tumors, which can cause compression. More rare and little described in the literature is the possibility of intestinal kaposiform hemangioma, which motivated the report of the case described [ 4 ].…”

“…It presents a better prognosis if it is limited to the intestine and not related to coagulopathies. It is characterized according to the malignancy as borderline, due to its rapid growth and invasion capacity [ 4 ].…”

“…An article describes a case that is similar to the one reported herein, in which the patient had abdominal distension and bilious vomiting. However, at 1 month old and presenting a vascular mass in the inoperative, it is the fifth reported case and the youngest patient so far [ 4 ]. Other forms of rare presentation include intussusception, obstruction and perforation [ 8 ].…”

“…The prognosis of the lesion takes into account its location and the possibility of resection and association with Kasabach-Merrit syndrome. No case described in the literature has presented an association with such syndrome [ 4 , 9 ].…”

Hemangiomas of Abdominal Organs in Children

“…Гемангиомы могут быть небольшими и могут достигать очень больших размеров, быть красного, синего цвета, бугристыми, консистенция плотная или мягко-эластичная. Достигая больших размеров гемангиома печени вы-зывает у детей чувство тяжести в эпигастральной области, общую слабость, иногда рвоту [10][11][12]…”