Isolated left ventricular noncompaction in association with rheumatic mitral stenosis

Atrial fibrillation in left ventricular noncompaction with and without neuromuscular disorders is associated with a poor prognosis

“…AF has been recently described as the first cardiac manifestation of dilated cardiomyopathy and quadriceps myopathy due to lamin A/C mutations [21]. In rare cases, AF might have developed due to rheumatic heart disease [22] or restrictive cardiomyopathy [23] ( Table 1).…”

Possible new syndrome: Left ventricular noncompaction, partial agenesis of the corpus callosum, and developmental delay in a Brazilian child

“…The isolated form of LVNC occurs in the absence of other structural heart disease, and the other form occurs in association with other congenital heart defects [Ichida et al, 2001; Markiewicz‐Łoskot et al, 2006; Xia et al, 2008]. Clinical and genetic heterogeneity have been clearly demonstrated since autosomal dominant, recessive, and X‐linked genes have been implicated as causal agents [Digilio et al, 1999; Sasse‐Klaassen et al, 2004; Brady et al, 2006; Xing et al, 2006; Stöllberger and Finsterer, 2007; Finsterer et al, 2008; Moric‐Janiszewska and Markiewicz‐Łoskot, 2008; Vijayvergiya et al, 2008]. LVNC has been frequently reported in association with several neuromuscular disorders [Bleyl et al, 1997; Finsterer et al, 2005; Stöllberger and Finsterer, 2005; Spencer et al, 2006; Finsterer et al, 2007a,b; Stöllberger et al, 2007].…”

Biventricular non-compaction — The rare cause of stroke in a young boy

“…Embolic complications as occurred in the index case are related with development of thrombi in the extensively trabeculated ventricle, depressed systolic function, and development of atrial fibrillation. The non-compaction area may be localized to left and or right ventricle [2,4,6]. Though the natural history of non-compaction is not very clear [5], the diagnosis is important for optimal medical treatment of both stroke and also underlying heart disease.…”