Metastatic Primitive Neuroectodermal Tumor of the Kidney in Adults

Casella, Roberto; Moch, Holger; Rochlitz, Christoph; Meier, Verena; Seifert, Bettina; Mihatsch, Michael J.; Gasser, Thomas C.

doi:10.1159/000052514

Cited by 62 publications

(37 citation statements)

References 20 publications

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“…In more advanced stages, the tumor involves the liver, spleen, peritoneum, and lungs. Th e prognosis for renal ES ⁄ PNET is generally poor, with a 5-year disease-free survival of 45% to 55% in localized cases, whereas cases with an advanced stage at presentation have a median relapse-free survival of only 2 years (9,13,15).…”

Section: Discussionmentioning

confidence: 99%

Primitive Neuroectodermal Tumors of the Kidney

Narayanan

Rajan

Preethi

2017

Baylor University Medical Center Proceedings

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Section: Discussionmentioning

confidence: 99%

Primitive Neuroectodermal Tumors of the Kidney

Narayanan

Rajan

Preethi

2017

Baylor University Medical Center Proceedings

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“…Despite aggressive treatment, prognosis remains poor. The median survival for advanced disease is only 2 years [15]. In a retrospective study, 31% patients had metastasis.…”

Section: Discussionmentioning

confidence: 99%

Ewings Sarcoma of the Kidney: A Rare Entity

Choubey

Pipara

Kumar

2017

World J Nephrol Urol

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Primary Ewings sarcoma (EWS) of the kidney is a very rare tumor and very few cases have been reported till date. We present a case of a young girl presenting to us with flank pain. On evaluation, she was found to have a renal mass. She was explored and a nephrectomy was done. Histopathology was reported as EWS. She was then planned for adjuvant chemotherapy. Primary EWS of the kidney is characterized by an aggressive course and poor prognosis. Hence, while dealing with renal masses in young patients, this entity should always be kept in mind.

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“…The 5-year disease-free survival rate is 45% to 55% and the median relapse-free survival is only 2 years in patients with metastatic disease. 8 Multimodal therapeutic approaches, consisting of surgical resection, chemotherapy and radiotherapy, are needed to treat this malignancy. rPNET tends to be very large and the tumour diameter is usually >10 cm.…”

Section: Discussionmentioning

confidence: 99%

Primitive neuroectodermal tumour of the kidney: An unusual case mimicking renal angiomyolipoma with minimal fat

Xie

Wen

et al. 2015

CUAJ

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Primitive neuroectodermal tumour (PNET) is a highly aggressive neoplasm that develops classically in the central nervous system. PNET of the kidney (rPNET) is extremely rare. Recently, a 23-yearold woman complained of left flank pain and intermittent hematuria for 3 months and was admitted to our hospital. A computed tomography (CT) scan and magnetic resonance imaging demonstrated a 5.1 × 4.4-cm heterogenous mass with unconspicuous reinforcement in the upper pole of the left kidney. F18-FDG positron emission tomography CT (PET-CT) revealed the mass as a benign lesion with internal extensive bleeding. Renal angiomyolipoma with minimal fat was diagnosed. Three months later, a CT scan showed that the mass shrank to 3.1 × 2.6 cm and nephron-sparing surgery of the left kidney was performed at the patient's request. However, histologic features and immunohistochemical analysis confirmed the diagnosis of rPNET. Five cycles of combined chemotherapy were executed. At the 11-month follow-up, the patient showed no evidence of metastasis or recurrence.

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Metastatic Primitive Neuroectodermal Tumor of the Kidney in Adults

Cited by 62 publications

References 20 publications

Primitive Neuroectodermal Tumors of the Kidney

Primitive Neuroectodermal Tumors of the Kidney

Ewings Sarcoma of the Kidney: A Rare Entity

Primitive neuroectodermal tumour of the kidney: An unusual case mimicking renal angiomyolipoma with minimal fat

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