Multiple non-syndromic odontogenic keratocysts in three siblings

Nirwan, Amit; Wanjari, Sangeeta; Saikhedkar, Rashmi; Karun, Vinayak

doi:10.1136/bcr-2012-007503

Cited by 2 publications

(5 citation statements)

References 12 publications

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“…OKC is well known for its high recurrence rate (HRR) and in patients with multiple OKC, a significant HRR of 30% has been reported compared to a solitary keratocyst. [4] As per Brannon et al [5] out of 312 cases of OKCs examined, 5.1% of the cases were associated with NBCCS and 5.8% of cases of multiple OKCs were non-syndromic. We hereby present a case of nonsyndromic multiple jaw cysts (NSMJCs) which was treated successfully by early detection and intervention.…”

Section: Introductionmentioning

confidence: 82%

Multiple Odontogenic Keratocysts in Nonsyndromic Patient-a Case Report

Banerjee,

Singh,

Sanjeeta

et al. 2024

PIJR

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Aim: This case report emphasizes the significant findings and presentation of a rare case of non-syndromic multiple jaw cysts (NSMJCs). Odontogenic keratocysts (OKCs) may occur either as solitary (non-syndromic OKCs) or Background: as multiple OKCs (syndromic OKCs). Multiple OKCs are usually linked with Gorlin–Goltz syndrome with features like skin carcinomas and bifid ribs, eye, and neurologic abnormalities. A non-syndromic 27-year-old Case Description: male patient presented with pain in his upper right back teeth region for 1 year, extraoral examination revealed swelling on the right side of the face. No other relevant findings were detected in the patient. Based on the clinical and radiological evaluation which revealed multiple OKCs. Enucleation was planned in all two quadrants and histopathological evaluation was performed. The patient was followed up multiple times for the duration of six months. Conclusion: Although our case fulfills only one of the major and none of the minor criteria of the syndrome, considering the reported literature and clinical presentation, early age, multiple OKC, involvement of both the jaws along with histological correlation, we propose our case to be a fractional expression of NBCCS. Any case Clinical significance: associated with single or multiple OKCs should be meticulously investigated locally and systemically for any other signs of NBCCS or other syndrome followed by a distinct treatment protocol depending on the patient's age, number, and size of the lesion, remaining subsequent growth, and proximity to adjacent vital structures, to provide a better quality of life with a minimal amount of morbidity and kept on strict regular follow-up.

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Section: Introductionmentioning

confidence: 82%

Multiple Odontogenic Keratocysts in Nonsyndromic Patient-a Case Report

Banerjee,

Singh,

Sanjeeta

et al. 2024

PIJR

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“…1. 38 casos -Somente aumento de volume 17,20,21,[23][24][25][26][28][29][30]35,[39][40][41][46][47][48]52,53,56,59,63,64,67,[70][71][72]75,81,89,92 ; 2. Aumento de volume associado a:…”

Section: Aspectos Clínicos Iniciaisunclassified

“…A maioria dos relatos de caso referiu ocorrência da lesão em mandíbula 8,11,14,[16][17][18][19][20][22][23][24][25]27,28,31,[33][34][35][36][37][39][40][41][42][43][45][46][47][48][49][50][51]53,54,56,58,59,61,65,67,[70][71][72]75,76,[78][79][80][82][83][84][85]…”

Section: Localizaçãounclassified

“…Tais dados são ratificados por MACDONALD-JANKOWSKI (2010) 93 . O lado direito foi o mais acometido [8][9][10]12,14,16,17,20,23,[25][26][27]30,32,33,[36][37][38][40][41][42][43]45,50,51,53,54,58,61,[63][64][65][66]72,75,78,79,81,84,[86][87][88][89]91 . Além disso, houve casos, nos quais a lesão era única com proporções extensas 28,31,36,39,58,82,…”

Section: Localizaçãounclassified

“…1. 42 casos -Somente enucleação 9,10,13,15,16,18,20,23,94,26,29,30,[44][45][46][47][48]50,52,53,57,59,60,62,65,[69][70][71]76,81,84,92 ; 2. Enucleação associada a: a.…”

Section: Tratamentounclassified

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Abordagem clínica e terapêutica sobre o Tumor Odontogênico Ceratocístico: uma revisão abrangente da literatura

Medeiros

Lombardo

Maito

et al. 2019

R. Fac. Odontol. Porto Alegre

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O Tumor odontogênico ceratocístico (TOC) é um tumor benigno intra-ósseo de origem odontogênica cuja prevalência corresponde a 11% das lesões císticas da maxila e mandíbula. Objetivo: realizar uma revisão da literatura sistematizada sobre o TOC. Metodologia: Foi realizada uma busca de relatos de caso clínico na base de dados PubMed sob os critérios: tipo de estudo (relato de caso), na língua inglesa, realizados apenas em humanos, sem limites de data de publicação. Resultados: Selecionou-se 85 artigos dos quais foram registrados os dados relevantes sobre os casos clínicos. Constatou-se que o TOC possui predileção por pacientes do sexo masculino, entre a terceira e quarta décadas de idade. Ocorre comumente em mandíbula, preferencialmente em região posterior. O aspecto clínico inicial mais frequente foi aumento de volume. Em relação aos aspectos imaginológicos, pode apresentar imagem radiolúcida única ou múltipla, uni ou multilocular. O exame histopatológico é fundamental para o diagnóstico. Teve enucleação como conduta terapêutica instituída na maioria dos casos. Em casos de múltiplas lesões, a investigação voltada para Síndrome de Gorlin-Goltz deve ser considerada. O tempo de acompanhamento, a taxa de recorrência e de transformação maligna foram variáveis. Considerações finais: É fundamental o exame histopatológico para o diagnóstico do Tumor odontogênico ceratocístico. A conduta terapêutica mais indicada é a enucleação associada a outro tratamento adjuvante. O acompanhamento periódico é mandatório visto o alto potencial de recorrência deste tipo de lesão.

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Multiple non-syndromic odontogenic keratocysts in three siblings

Cited by 2 publications

References 12 publications

Multiple Odontogenic Keratocysts in Nonsyndromic Patient-a Case Report

Multiple Odontogenic Keratocysts in Nonsyndromic Patient-a Case Report

Abordagem clínica e terapêutica sobre o Tumor Odontogênico Ceratocístico: uma revisão abrangente da literatura

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