Papillon-Lefevre syndrome: A case report of four affected siblings

Angel, Tiffany A.; Hsu, Sylvia; Kornbleuth, Steven I.; Kornbleuth, Joseph; Kramer, E.Michael

doi:10.1016/s0190-9622(02)70220-x

Search citation statements

Order By: Relevance

Paper Sections

Select...

Discussion2

Citation Types

Supporting

Mentioning

Contrasting

Year Published

2005

2010

Publication Types

Select...

Article2

Book1

Relationship

Self Cite0

Independent3

Authors

Journals

Cited by 3 publications

(2 citation statements)

References 16 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…8 Clinically, patients present with bleeding gums, erythema, suppuration, and inflammation, which eventually leads to premature loss of the permanent teeth.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Papillon‐Lefèvre Syndrome: A Successful Outcome

Ahuja¹,

Shin²,

Mudgil³

et al. 2005

Journal of Periodontology

View full text Add to dashboard Cite

show abstract

“…8 Clinically, patients present with bleeding gums, erythema, suppuration, and inflammation, which eventually leads to premature loss of the permanent teeth.…”

Section: Discussionmentioning

confidence: 99%

“…In PLS, the destruction to the periodontium is severe and commences early in life at approximately 1 to 4 years of age. 8 Clinically, patients present with bleeding gums, erythema, suppuration, and inflammation, which eventually leads to premature loss of the permanent teeth.…”

Section: Discussionmentioning

confidence: 99%

Papillon‐Lefèvre Syndrome: A Successful Outcome

Ahuja¹,

Shin²,

Mudgil³

et al. 2005

Journal of Periodontology

View full text Add to dashboard Cite

show abstract

9 Disorders of epidermal maturation and keratinization

2010

Weedon's Skin Pathology

View full text Add to dashboard Cite

Late‐onset Papillon–Lefevre syndrome with pyogenic liver abscesses: report of one case

Yazdanfar

Farahnaki

2008

Int J Dermatology

View full text Add to dashboard Cite

A 25‐year‐old woman living in Hamedan, Iran, presented originally at 7 years of age with erythematous, hyperkeratotic lesions on the palms and soles with extension to the dorsal side of the hands and feet. Involvement of the elbows and knees was also seen. From 12 years of age, she started to lose her teeth. At the same age, she experienced fever, chills, malaise, myalgia, and right upper quadrant abdominal pain. With a diagnosis of pyogenic liver abscesses, the patient underwent successful surgical treatment. Examination revealed erythematous, hyperkeratotic, scaling plaques on the palms and soles, dorsal side of the hands and feet (Fig. 1), elbows and knees. All the teeth were missing from the mouth (Fig. 2), and she used a dental prosthesis. A surgical scar was observed on the right upper quadrant of the abdomen (Fig. 3). Skull X‐ray and computed tomography scan were normal. Skin biopsy of the dorsal right hand demonstrated hyperkeratosis, focal parakeratosis, hypergranulosis, and acanthosis with a mild inflammatory infiltrate around the vessels (Fig. 4). 1 Hyperkeratotic plaques on the hands and feet 2 Loss of permanent teeth 3 Surgical scar on the right upper quadrant of the abdomen and hyperkeratotic plaques on the hand 4 Hyperkeratosis, focal parakeratosis, hypergranulosis, and acanthosis (hematoxylin and eosin, ×40)

show abstract

Papillon-Lefevre syndrome: A case report of four affected siblings

Cited by 3 publications

References 16 publications

Papillon‐Lefèvre Syndrome: A Successful Outcome

Papillon‐Lefèvre Syndrome: A Successful Outcome

9 Disorders of epidermal maturation and keratinization

Late‐onset Papillon–Lefevre syndrome with pyogenic liver abscesses: report of one case

Contact Info

Product

Resources

About