Aim: To determine the pattern of congenital heart diseases among children presenting to tertiary care hospital. Material and Methods: A cross sectional study was carried out at Department of Paediatrics Cardiology, National institute of Cardiovascular Disease Karachi in the duration from November, 2022 to April, 2023. Total 171 patients were presented with CHD. Patients aged between 1 to 12 months of both genders. Pattern of CHD among the patients was determined. Results: Acyanotic CHD was seen in 74.26% patients. Cyanotic CHD was seen in 25.73% patients. Atrial Septal Defect (48.8%) was the most common presentation in acyanotic CHD patients while Tetralogy of Fallot was common presentation (40.9%) in cyanotic CHD patients. Conclusion: From our study we conclude that majority of the patients had acyanotic CHD as compared to cyanotic CHD, Ventricular Septal Defect and Atrial Septal Defect were more prevalent in cyanotic CHD while Tetralogy of Fallot was more common in cyanotic CHD.