Prader-Willi Syndrome: A Case Report

Tayal, Erika; Indushekar, K R; Saraf, Bhavna G; Sheoran, Neha; Doda, Ashima

doi:10.17140/phoj-1-104

Cited by 4 publications

(3 citation statements)

References 7 publications

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“…Once the diagnosis of the syndrome is confirmed, dental appointments should be initiated in a collaborative work with parents to inform about the possible dental problems and instructions of how to avoid them. The early introduction of healthy nutrition and oral hygiene practices and the use of fluoride supplements, when appropriate, would help to avoid deleterious dental consequences [ 20 ].…”

Section: Discussionmentioning

confidence: 99%

Special Care Dentistry in a Patient with Prader–Willi Syndrome through the Use of Atraumatic Restorative Treatment under General Anesthesia

Roman-Torres

Kussaba

Bantim³

et al. 2017

Case Reports in Dentistry

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Prader–Willi syndrome described in 1956 has a genetic origin, affecting both genders, varying in presence and intensity from individual to individual. A precocious diagnosis, before the manifestation of symptoms, has brought some improvement in the quality of life of the carriers in the last years. The objective of this case report was to describe the treatment realized in a 3-year-old boy who presented grade II obesity, difficulty of locomotion, hypotonia, and history of cardiopathy. A dental treatment under general anesthesia was defined, allowing an oral adequation in a single section, in which it was planned the extraction of the element 74 and atraumatic restorative treatment (ART) technique in the other teeth. The precocious intervention in this 3-year-old patient by the therapy realized with ART under general anesthesia was done with success, avoiding unnecessary extractions, preserving dental elements, and maintaining the oral cavity in adequate function.

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Section: Discussionmentioning

confidence: 99%

Special Care Dentistry in a Patient with Prader–Willi Syndrome through the Use of Atraumatic Restorative Treatment under General Anesthesia

Roman-Torres

Kussaba

Bantim³

et al. 2017

Case Reports in Dentistry

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“…A variety of oral diseases are found in patients with PWS (Table 2) such as caries,1,17,21,25–31 hypoplastic enamel,1,17,25,28,31 viscous saliva,1,17,21,25,30–32 periodontal disease,25–28 tooth wear,1,26,27,31,32 dental erosion,33 rampant caries,1,29,31 oral microsomia,25,31 dental malocclusion,1,17,21,26–29 candidiasis,25,27 erythematous lesions of the oral mucosa,27 increased biofilm accumulation,1,21,25,31,32 gingivitis,1,25,27,31,32 angular cheilitis, dry mouth,28 demineralization,21,25,31 dentoalveolar abscess,29,31 hypotonic tongue,21,31 mouth breathing,21,31,32 root stumps30 and a delay in tooth eruption 28Table 2Oral manifestation, referenceOral manifestation Júnior et al, 2005Scardina; Fuca; Messina, 2007Bailleuil-Forestier et al, 2008Yanagita et al, 2011Witt et al, 2011Setti et al, 2012Gardens et al, 2014Song et al, 2015Hurren, Flack, 2016 (review)Tayal et al, 2016Roman-Torres et al, 2017Olczak-Kowalczyk et al, 2018*…”

Section: Introductionmentioning

confidence: 99%

“…Besides this, delayed tooth eruption in a 10-year-old boy was observed to conform with periapical and panoramic radiographic examination 28. Delayed healing of wounds was reported after the extraction of teeth 30…”

Section: Introductionmentioning

confidence: 99%

<p>Oral health in patients with Prader-Willi syndrome: current perspectives</p>

Bantim¹,

Kussaba²,

Carvalho³

et al. 2019

CCIDE

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Prader-Willi syndrome (PWS) is a rare complex multisystem disorder and presents several aspects related to dentistry. The purpose of this review is to present current perspectives about oral health in patients with PWS. Delay development, hyperphagia, foamy and highly viscous saliva raise the risk of caries and contribute to tooth wear. Cariogenic foods uncontrolled consumption allows to obesity and dental problems progress worsening systemic disorders. These factors can be controlled. The success in follow-ups with caries free and oral health controlled demonstrate the importance of multidisciplinary team intervention corroborated by support at home from birth to adulthood. Thereby, current perspective on the disease is that there is possibility of proper maintenance of oral health in PWS patients. Guided care interferes positively with the overall well-being and quality of life of the individual with PWS and their family. A multidisciplinary team with a focus on teaching patients and family members will help minimize eventual problems.

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Prader Willi Sendromlu Hastada Genel Anestezi Altında Diş Tedavisi: Olgu Sunumu

GÜRSOY>

2022

Selcuk Dental Journal

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Prader-Willi sendromu (PWS), karakteristik yüz görünümü, gelişim geriliği, kısa boy, küçük el ve ayaklar, infantil hipotoni, anormal cinsel olgunlaşma ile hipogonadizm, mental retardasyon ve davranış bozuklukları ile karekterize nadir görülen bir sendromdur. Hiperfajinin tetiklediği yüksek çürük riski olan PWS’li hastaların, küçük çene yapısı ve iletişim kurmayı engelleyen mental problemleri nedeniyle klinik şartlarda lokal anestezi altında diş tedavi uygulamalarının ciddi zorluklar içerdiği rapor edilmektedir. PWS’li olgularda hipotoni, küçük çene yapısı ve kısıtlı boyun hareketliliği, genel anestezi sırasında havayolu yönetiminde ciddi zorluklara neden olduğu bilindiğinden bu hastalarda en kötü senaryoya göre hazırlıkların yapılması ve hastanın operasyon sırasında yakın takip altında tutulması gerekmektedir. Bu olgu sunumunda; genel anestezi ile dental tedavi uygulanan PWS’li bir hasta ve alınması gereken önlemler sunulmuştur.

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Prader-Willi Syndrome: A Case Report

Cited by 4 publications

References 7 publications

Special Care Dentistry in a Patient with Prader–Willi Syndrome through the Use of Atraumatic Restorative Treatment under General Anesthesia

Special Care Dentistry in a Patient with Prader–Willi Syndrome through the Use of Atraumatic Restorative Treatment under General Anesthesia

<p>Oral health in patients with Prader-Willi syndrome: current perspectives</p>

Prader Willi Sendromlu Hastada Genel Anestezi Altında Diş Tedavisi: Olgu Sunumu

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