Prednisolone for pulmonary hemorrhage after Fontan procedure

Abstract

An 8-year-old boy with tricuspid atresia (type 2C), who underwent Damus-Kaye-Stansel and Fontan procedures (extracardiac conduit) by the age of 3 years, presented with severe exertional dyspnea. Aortic valve replacement and atrioventricular valvuloplasty after Fontan procedure were also performed 6 months prior to the current presentation. The dyspnea developed over a few days, and he was admitted to the present hospital with an oxygen saturation of 70%, down from his usual 95%. Blood sampling indicated anemia, with a hemoglobin level of 9.2 g/dL. On chest X-ray and computed tomography (CT), the bilateral lung fields had a diffuse ground-glass