Primary Ewing's sarcoma/Primitive neuroectodermal tumour of the kidney: Report of four cases from a tertiary care centre.

Kar, Shreya; Shah, Saloni Naresh; Menon, Maya; Narayanan, Geetha

doi:10.1016/j.cpccr.2020.100043

Cited by 2 publications

(7 citation statements)

References 2 publications

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“…The differential diagnosis includes other round cell tumors of kidney including Wilms tumor/ nephroblastoma, neuroblastoma, renal cell carcinoma, malignant lymphoma, desmoplastic small round cell tumor, clear cell sarcoma, synovial sarcoma and metastatic small round cell tumor from other site. 11,12 This differential diagnosis is further complicated by the overlapping morphological features and the relatively rare occurrence of most of these entities in the kidney. 10 Reportedly, renal PNET usually occur in young adults with a mean age of 30.5 years having 66.7% male predominance.…”

Section: Discussionmentioning

confidence: 99%

Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Jannat¹,

Doly²,

Sharif³

et al. 2023

Khwaja Yunus Ali Medical College Journal

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Renal primitive neuroectodermal tumor (renal PNET) or renal Ewing sarcoma (renal ES) is a rare, rapidly growing malignant small round cell tumor with poor prognosis. A 32-years-old Bangladeshi male patient presented with right loin pain, fever and anemia. On CT imaging a large (18x10.5x10.0 cm) renal mass was discovered. On suspicion of malignancy, a biopsy was taken from the mass. Microscopic evaluation showed features consistent with malignant small round blue cell tumor. Immunohistochemical stains showed diffuse and strong positive reaction to CD-99 and negative for WT-1, CD-3 and CD-20, which confirmed the diagnosis of renal PNET. After 6 cycles of combined chemotherapy, the patient was relatively well and at 6 months follow-up he showed no evidence of metastasis or recurrence. KYAMC Journal Vol. 13, No. 04, January 2023: 257-260

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Section: Discussionmentioning

confidence: 99%

Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Jannat¹,

Doly²,

Sharif³

et al. 2023

Khwaja Yunus Ali Medical College Journal

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“…Primary ES of the kidney typically manifests in children and adolescents with a strong male predilection [4].…”

Section: Discussionmentioning

confidence: 99%

“…ES is an aggressive osseous and soft tissue tumor in children and young adults. Even though primary ES of the retroperitoneum, pelvis, and visceral organs is rare, they have been described in the literature [ 4 ]. The first case of primary ES of the kidney was reported by Seemayer et al in 1975.…”

Section: Discussionmentioning

confidence: 99%

“…Primary ES of the kidney typically manifests in children and adolescents with a strong male predilection [ 4 ]. The clinical presentations of these patients include flank/abdominal pain, palpable mass, and hematuria [ 6 ].…”

Section: Discussionmentioning

confidence: 99%

“…Usually, they remain asymptomatic for a long time, until the mass reaches a palpable size, as seen in our case. These tumors usually arise from the medullary or pelvic region and can involve the entire kidney with invasion into the renal vein and inferior vena cava [ 4 ]. In our case, the tumor extensively involved the entire left kidney with compression of the common iliac vein, accounting for the swelling of the left lower limb.…”

Section: Discussionmentioning

confidence: 99%

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Primary Adult Renal Ewing’s Sarcoma: A Rare Entity

Shangpliang¹,

Rangad²,

Das³

et al. 2022

Cureus

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Ewing's sarcoma/primitive neuroectodermal tumors are high-grade small round blue cell tumors traditionally found in children and adolescents. These tumors primarily affect the bone and soft tissue, with extraskeletal sites rarely being affected. The clinical presentation and imaging findings are non-specific and are not characteristic. The diagnosis is essentially based on the histopathologic findings assisted by immunohistochemistry and/or cytogenetic molecular studies. Proper diagnoses and timely management of this tumor are essential owing to the aggressive nature and poor prognosis of the disease.

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Primary Ewing's sarcoma/Primitive neuroectodermal tumour of the kidney: Report of four cases from a tertiary care centre.

Cited by 2 publications

References 2 publications

Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Primary Adult Renal Ewing’s Sarcoma: A Rare Entity

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