Primary Extraskeletal Mesenchymal Chondrosarcoma Arising from the Pancreas

Oh, Bae-Geun; Han, Yoon Hee; Lee, Byung‐Hoon; Kim, Su Young; Hwang, Yoon Joon; Seo, Jiwon; Kim, Yong Hoon; Joo, Soon; Hur, Gham; Joo, Mee

doi:10.3348/kjr.2007.8.6.541

Cited by 20 publications

(24 citation statements)

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“…Las localizaciones frecuentes incluyen: tejidos blandos de la órbita, cerebro, meninges y extremidades inferiores, especialmente a nivel del muslo (4)(5)(6)(7)(8) . El mediastino, retroperitoneo y riñón son localizaciones menos frecuentes (4,6) .…”

Section: Discussionunclassified

“…El mediastino, retroperitoneo y riñón son localizaciones menos frecuentes (4,6) . El CME es más frecuente en mujeres, con presentación bimodal; presenta dos momentos de mayor incidencia, el primero en la tercera década, comprometiendo cabeza y cuello, y el segundo en la quinta década con predilección por los tejidos blandos, especialmente el muslo (4,9,10) .…”

Section: Discussionunclassified

“…El compromiso metastásico es más común en el adulto generalmente a pulmón y nódulos linfáticos, con alta tasa de recidiva local y mayor mortalidad (1,4,11) . La sobrevida a 5 años es de 42 -56% y a 10 años de 28%, reportando recurrencias o metástasis 10 a 20 años posterior al diagnóstico (6) . El manejo inicial es la resección quirúrgica de la masa.…”

Section: Discussionunclassified

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C0ndr0sarc0ma Mesenquimal Extraesquelético en Un Paciente Pediátrico: Revisión De La Literatura a Propósito De Un Caso

H¹,

V²,

R³

et al. 2010

Rev. chil. radiol.

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The extraskeletal mesenc hymal chondrosarcoma belongs to a group of infrequent malignant cartilaginous tumors, which are not obvious mainly in the bone. The most common site of such tumors is within the orbit, the central nervous system and the soft tissues of the lower limbs. The commitment is usually metastatic to the lung and lymph nodes IntroducciónEl condrosarcoma mesenquimal extraesquelético (CME) corresponde al 1-2% de todos los tumores malignos de los tejidos blandos y constituye una variante infrecuente y agresiva del condrosarcoma (1,2) . El abordaje imaginológico incluye: radiografía convencional, tomografía computada (TC) y resonancia magnética (RM), que permiten caracterizar la estructura interna de la masa y establecer el grado de compromiso de los tejidos blandos subyacentes así como eventual extensión ósea.El artículo tiene como objetivo presentar el caso de un paciente de sexo masculino de 14 años de edad, que ingresó a nuestra institución con una lesión sólida localizada a nivel de los tejidos blandos en el aspecto posterior de la pierna derecha y cuyo estudio histopatológico confirmó un CME; a propósito del caso, efectuamos la revisión bibliográfica del tema.Caso clínico. Paciente masculino de 14 años de edad que consultó por dolor en la pierna derecha de 2 meses de evolución posterior a trauma, refieriendo sensación de masa en esa localización de 2 años de evolución.Inicialmente es evaluado con radiografía simple donde se identifica una masa en los tejidos blandos del aspecto posterior de la pierna derecha, de matriz calcificada, con patrón condroide. No se observa compromiso óseo subyacente (Figura 1

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C0ndr0sarc0ma Mesenquimal Extraesquelético en Un Paciente Pediátrico: Revisión De La Literatura a Propósito De Un Caso

H¹,

V²,

R³

et al. 2010

Rev. chil. radiol.

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“…Matrix mineralization is more common in EMCS but calcifications may not be evident in rare instances [21]. On contrast enhancement the tumor appears lobulated with peripheral enhancement and sometimes with central low attenuation areas that probably represent necrosis [5,22]. The uncalcified areas have low attenuation similar to muscle on CT [20].…”

Section: Discussionmentioning

confidence: 99%

A Rare Case of Extraskeletal Mesenchymal Chondrosarcoma with Dedifferentiation Arising from the Buccal Space in a Young Male

Gupta

Sharma

et al. 2013

J. Maxillofac. Oral Surg.

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Extraskeletal mesenchymal chondrosarcoma (EMCS) is a rare and aggressive pathological variant of chondrosarcoma arising from soft tissues of mainly the extremities, meninges/dura, trunk, and orbits. EMCS comprises only 2 % of all soft tissue sarcomas and only 6 % of them arise from soft tissue in the head and neck region. It usually affects in the second and third decade of life and is common in women. It runs a very rapid clinical course with distant metastases and has poor prognosis and survival rates. Histologically it has a dimorphic presentation of small round mesenchymal cells interspersed with foci of cartilaginous differentiation. Radiographically it appears as a soft tissue lobulated mass with various patterns of calcification. This is the first case of primary and recurrent EMCS originating in the buccal space with unusual features of dedifferentiation. The diagnostic challenges in this case were the inconclusive FNAC results, lack of radiographic evidence of characteristic calcifications and presence of areas of myxoid material and dedifferentiation on histopathology. The clinical, cytological, histological, immunohistochemical, radiographic, PET-CT findings and management with review of literature is presented. The diagnostic and management pitfalls of this extremely rare tumor are also discussed.

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“…7 Primary pancreatic chondrosarcoma is extremely rare; there has been only one other case reported in the literature. 3 Histological classification of chondrosarcoma includes myxoid, mesenchymal, and dedifferentiated types. Mesenchymal chondrosarcoma was first reported by Lichtenstein and Bernstein 8 in 1959, and extraskeletal mesenchymal chondrosarcoma in soft tissues was reported by Dowling 9 in 1964.…”

Section: Discussionmentioning

confidence: 99%

Primary mesenchymal chondrosarcoma of the pancreas

Dai

2010

annals

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Extraskeletal chondrosarcomas are rare and there is only one reported case of primary pancreatic chondrosarcoma. We report the case of a 34-year-old woman with a 6-month history of abdominal pain and distention. Radiological studies indicated a mass in the pancreas, and exploratory laparotomy revealed a tumour of the pancreas extending to the hepatic vessels and hepatoduodenal ligament. The mass was completely excised, and the histopathological diagnosis was primary mesenchymal pancreatic chondrosarcoma. Tumour recurred at follow-up 52 months postoperatively.

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Primary Extraskeletal Mesenchymal Chondrosarcoma Arising from the Pancreas

Cited by 20 publications

References 7 publications

C0ndr0sarc0ma Mesenquimal Extraesquelético en Un Paciente Pediátrico: Revisión De La Literatura a Propósito De Un Caso

C0ndr0sarc0ma Mesenquimal Extraesquelético en Un Paciente Pediátrico: Revisión De La Literatura a Propósito De Un Caso

A Rare Case of Extraskeletal Mesenchymal Chondrosarcoma with Dedifferentiation Arising from the Buccal Space in a Young Male

Primary mesenchymal chondrosarcoma of the pancreas

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