yda tid cyst in fec ti on is one of the ol dest di se a ses known in the history of hu ma nity.1 Hyda tid cyst is a di se a se ca u sed by the lar val Echi no coc cus gra nu lo sus ta pe worm [2][3][4][5] and is se en in re gi ons whe re pa ra si tic in fes ta ti ons are en de mic. 4,6 Ani mals are ma in cul prits in the spre ad It is a disease caused by the larval Echinococcus granulosus tapeworm and is seen in regions where parasitic infestations are endemic. Spinal hydatid disease is an infestation characterized by multivesicular diffuse infiltration of the cancellous bone, including corpus vertebrae, pedicles, and the lamina. This is a rare condition leading to severe neurological problems. In the spinal area, the most commonly involved part is the thoracic region. Diagnosis is difficult and frequently delayed until signs and symptoms of spinal cord and nerve compression develop. There are no characteristic signs and symptoms. Most common signs are low back pain, radicular pain, paraparesis or paraplegia, sensation disorders, and bladder/intestine dysfunction. Magnetic resonance imaging (MRI) is the most sensitive diagnostic method. In the treatment of spinal hydatid cyst, surgery is still accepted as the "gold standard". Antihelmintic agents and benzimidazole derivatives can also be combined with surgical treatment, particularly for preventing recurrences. After review of the related literature, it is emphasized that physicians should be careful in the differential diagnosis of patients applying with spinal pain, radicular pain, progressive myelopathy or spinal cord compression syndrome. Because of high mortality and morbidity; importance of early diagnosis and treatment is highlighted along with emphasizing eradication of disease.