Primitive neuroectodermal tumor of the kidney.

Malignant peripheral neuroectodermal tumor (MPNET) of the kidney

“…Some of these tumors are also found at the level of the thoracopulmonary wall (Askin tumors) and less commonly in the paravertebral area. A renal origin has been described, to our knowledge, only in eight previous cases [7,8]. The most typical gross pathologic and radiographic features include large size, lack of extensive parenchyma infiltration, lack of renal vein invasion, diffuse large calcifications, areas of internal hemorrhage and necrosis, and peripheral hypervascularity [5][6][7][8].…”

“…To our knowledge, there have been a few pathologic reports of this entity [5][6][7] and only one previous radiologic description [8]. In this report, we describe the main radiological and pathologic features in a patient with MPNET of the kidney.…”

Primitive neuroectodermal kidney tumour

“…Primitive neuroectodermal tumour has been described as having a lack of renal vein involvement 1−4 . To our knowledge, the present case is the first case with the tumour thrombus extending up to pulmonary infundibulum.…”

“…Almost all the cases of renal PNET were diagnosed after nephrectomy, but the survival rates and the prognosis of the renal PNET patients are generally considered poor with or without surgery 1 .…”

“…Extracranial PNET, particularly renal in origin, is extremely rare. Only four cases of renal origin have been described radiologically but using either one or two imaging techniques only 1−4 . We report a rare case of PNET of the kidney in a teenager and describe the sonographic, CT and MRI findings, and demonstrate the importance of biopsy for further management.…”