Pseudomyxoma extraperitonei: a rare presentation of a rare tumour

Diaz-Zorrilla, Carmina; Medina, Antonio Ramos-De la; Grube-Pagola, Peter; Velasco, Alfredo Ramírez Gutiérrez de

doi:10.1136/bcr-2012-007702

Cited by 5 publications

(8 citation statements)

References 26 publications

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“…The reported 5-year survival of patients with pseudomyxoma peritonei ranges from 11% to 75% (mean: 50%) (1). Due to the scarcity of reported cases, the survival rates are not well known in pseudomyxoma retroperitonei, but appear to be better than pseudomyxoma peritonei, since the disease is confined to the retroperitoneum, and the vital organs are not involved (1,6).…”

Section: Discussionmentioning

confidence: 99%

“…Usually, the organ of origin is the appendix, with other rare primary sites being the ovaries, colon, stomach, pancreas, uterus, common bile duct and urachus (1,6). Rarely, a gelatinous pseudomyxoma is confined exclusively to the retroperitoneal compartment and, accordingly, is termed pseudomyxoma retroperitonei.…”

Section: Discussionmentioning

confidence: 99%

“…Rarely, a gelatinous pseudomyxoma is confined exclusively to the retroperitoneal compartment and, accordingly, is termed pseudomyxoma retroperitonei. A retrocaecal appendix accounts for the majority of such cases, but mucinous neoplasms of the ovary, ascending colon and rectum have also been implicated in its aetiology (1,(8)(9)(10). The primary mucous secreting neoplasms of the appendix may range from a low grade cystadenoma to a malignant cystadenocarcinoma (4).…”

Section: Discussionmentioning

confidence: 99%

“…In the present case, the unique retrocaecal positioning of the appendix facilitated its rupture into the retroperitoneal space, with a resultant PMR. A preoperative diagnosis of pseudomyxoma remains frustratingly elusive, since they can remain asymptomatic for long periods of time, and when symptomatic, the features are nonspecific, such as an abdominal mass, pain and weight loss (1,4).…”

Section: Discussionmentioning

confidence: 99%

“…Pseudomyxoma retroperitonei (PMR) is a rare condition, characterised by a mucinous collection in the retroperitoneum, with only 45 documented cases having been reported in the English literature (1). The most common presentation of PMR is an abdominal mass with pain, while three cases have presented with spontaneous cutaneous fistulae (2)(3)(4), and only a single case exhibited a mass in the anterior thigh region (5).…”

Section: Introductionmentioning

confidence: 99%

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Rare Presentation of Pseudomyxoma Retroperitonei: Stretching the Limits

Hasan

Kumar

Rao

et al. 2016

MJMS

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A 55-year-old woman presented with a mucopurulent sinusal discharge from the right supragluteal region, with symptoms over the previous five months. This abscess began as a slowly swelling growth, which eventually turned into a discharging sinus, and she was diagnosed with a gluteal abscess. The patient underwent incisional drainage, and intra-operatively, the sinus tract could be seen extending to the retroperitoneum. A subsequent CT scan and an MRI of the abdomen revealed a large heterogeneous retroperitoneal cystic mass on the right side of midline, extending inferiorly into the anterior thigh along the iliopsoas. Superiorly, a tubular projection extended from the lesion, indenting the ileocaecal junction, while a fluid filled cutaneous fistulous tract was seen, extending to the right flank. A diagnosis of pseudomyxoma retroperitonei, likely of retrocaecal appendicular origin, was proposed. An explorative laparotomy with an appendectomy, and the evacuation of the retroperitoneal collection were completed. The subsequent histopathology confirmed the diagnosis of appendicular mucinous cystadenoma, with pseudomyxoma retroperitonei.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

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Rare Presentation of Pseudomyxoma Retroperitonei: Stretching the Limits

Hasan

Kumar

Rao

et al. 2016

MJMS

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A retroperitoneal pseudomyxoma of the appendix: A case report

Atri,

Rany,

Hammami

et al. 2024

International Journal of Surgery Case Reports

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A Rare Case of Psoas Abscess Secondary to Mucinous Adenocarcinoma of the Appendix: A Case Report

Prabhu¹,

Koshire²,

Khandelwal³

2021

JOCR

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Introduction: Iliacus and psoas muscles are located in an extraperitoneal location forming the iliopsoas compartment. Iliopsoas abscess is a myositis involving this compartment. Pseudomyxoma peritonei is characterized by an abundant extracellular collection of mucin in the peritoneal cavity. When this collection is retroperitoneal, it is termed as pseudomyxoma extraperitonei. We present to you the case of a 52-year-old female with psoas abscess secondary to mucinous adenocarcinoma of the appendix, which was later diagnosed as pseudomyxoma extraperitonei. Case Presentation: A 52-year-old female presented with pain in the right flank with discharging sinuses since one year. She had previously undergone two surgeries in the past 1 year for drainage of the abscess and had taken first line anti-tubercular treatment for around 6 months. She was managed in our institute by an open drainage of the abscess. The culture reports showed an infection with E. coli. The histopathology sections showed abundant pools of extracellular mucin with strips of columnar epithelium which indicated the pathology to be a mucinous adenocarcinoma. A contrast-enhanced computed tomography scan of the abdomen and pelvis showed a ruptured appendix mucocele and a collection in the right psoas muscle showing fistulous communication with the cecum and extending to the suture site in the right flank. Anti-tubercular treatment was stopped and an oncology opinion was taken. The patient was managed with a palliative ileostomy. Conclusion: It is important to keep in mind diagnostic possibilities other than tuberculosis of the spine when managing a patient with an iliopsoas abscess. These include pathologies of the gastrointestinal and genitourinary tract, which need to be diagnosed and managed early. Keywords: Psoas abscess, pseudomyxoma peritonei, pseudomyxoma extraperitonei, mucocele of appendix, mucinous adenocarcinoma.

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Pseudomyxoma extraperitonei: a rare presentation of a rare tumour

Cited by 5 publications

References 26 publications

Rare Presentation of Pseudomyxoma Retroperitonei: Stretching the Limits

Rare Presentation of Pseudomyxoma Retroperitonei: Stretching the Limits

A retroperitoneal pseudomyxoma of the appendix: A case report

A Rare Case of Psoas Abscess Secondary to Mucinous Adenocarcinoma of the Appendix: A Case Report

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