Recurring adventitial cyst in the left external iliac vein

Han

et al. 2020

VSI

Adventitial cystic disease (ACD) is a very rare condition characterized by the accumulation of a cyst filled with gelatinous substance in the adventitia of a vessel adjacent to the joint area. The cyst usually compresses the vessel lumen, causing claudication or leg swelling. The disease usually affects the popliteal artery. However, several cases of venous ACDs particularly in the common femoral or external iliac vein have been reported. The definition, diagnosis, and optimal treatment of ACD remain controversial because of its rarity and the inconsistent use of terminology. The heterogeneity of the reported cases is more prominent in venous ACD. Herein, the accurate terminology of cysts correlated to the joint (synovial cyst, ganglion cyst, and adventitial cyst) and the pathogenesis, anatomy, and optimal therapy of venous ACD are discussed in detail to establish reporting standards for future studies.

Section: Treatment Of Cystic Diseases Around the Jointsmentioning

confidence: 99%

Inconsistent Use of Terminology and Different Treatment Outcomes of Venous Adventitial Cystic Disease: A Proposal for Reporting Standards

Han

et al. 2020

VSI

Journal of Vascular Surgery

“…There are only 32 reported cases of ACD of the vein in the world literature, including this case. [1][2][3][4][5][6][7][8][9][10][11][12][13][14][15][16][17][18] In contrast, adventitial cystic disease of the artery is a well-described, if rare, cause of intermittent lower extremity arteriogenic claudication occurring in 1:1200 cases of claudication. 19,20 ACD of the artery involves the popliteal artery in 85% of cases.…”

Section: Discussionmentioning

confidence: 94%

“…1,5,6,10 In 13 cases, cyst excision was attempted at the initial operation and recurrence occurred in only 3 patients. 4,8,13 Recurrence has been attributed to incomplete excision of cystic tissue; significant portions of the cyst are left in situ and may continue to secrete mucinous material. A more contemporary option is resection of the affected portion of the vein and immediate reconstruction with prosthetic or autologous graft as performed in 5 cases.…”

Section: Discussionmentioning

confidence: 99%

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Adventitial cystic disease of the femoral vein in a 5-year-old boy mimicking deep venous thrombosis

Jones

Rezayat

Winchester

et al. 2012

Adventitial cystic disease of the vein is a rare vascular anomaly with 32 reported cases. A 5-year-old boy initially presented with painless leg swelling. He was misdiagnosed with deep vein thrombosis and treated with 3 months of warfarin. When swelling failed to improve, a magnetic resonance venogram showed a mural cystic lesion of the left common femoral vein. In the operating room, the cyst was excised, relieving the obstructive effect and restoring flow. The swelling resolved within days. This is the first reported case of adventitial cystic disease of the vein occurring in a pediatric patient.

“…Since the earliest reports, this disease has been considered equivalent with the adventitial cystic disease of the arteries (6). The cysts in both types of vessels show slow growth and a tendency to recur after treatment.…”

Section: Discussionmentioning

confidence: 99%

Adventitial Cystic Disease of the Femoral Vein: a Case Report with the CT Venography

2009

Fewer than 20 cases of adventitial cystic disease of the vein have been reported in the worldwide literature. This small number of reported cases may be due not only to the disease's low incidence, but also to the difficulty in making the proper diagnosis. Many techniques have been used to investigate this disease, but venography has been the traditional diagnostic tool. In this report we present a case of adventitial cystic disease that was well demonstrated by CT venography.