Respiratory problems and cystic adenomatoid malformation of lung.

Walker, J.T.; Cudmore, R.E.

doi:10.1136/adc.65.7_spec_no.649

Cited by 20 publications

(15 citation statements)

References 5 publications

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“…Foram identificados 15 recém-nascidos, nove do sexo feminino, seis do sexo masculino, com a mediana do peso ao nascimento nos 3100 g (645--3975) e da idade gestacional nas 38 semanas (24)(25)(26)(27)(28)(29)(30)(31)(32)(33)(34)(35)(36)(37)(38)(39)(40). A distribuição do número de casos por centro foi a seguinte: Hospital de São João = 4; Hospital Geral de Santo António = 3 7 ; Centro Hospitalar de Vila Nova de Gaia = 4; Hospital Pedro Hispano = 1; Maternidade Júlio Dinis = 3.…”

Section: Resultsunclassified

“…Resultados: Foram identificados 15 recém-nascidos, 9F/6M, peso ao nascimento 3100 g (645-3975), idade gestacional de 38 semanas (24)(25)(26)(27)(28)(29)(30)(31)(32)(33)(34)(35)(36)(37)(38)(39)(40). A incidên-cia de MACPC foi de 1:9300 nascimentos.…”

Section: Malformação Congénita Das Vias Aéreas Pulmonares -Experiênciunclassified

“…A incidên-cia de MACPC foi de 1:9300 nascimentos. Onze (73%) recém-nascidos apresentaram diagnóstico pré-natal de lesão pulmonar cística pelas 22 semanas (19)(20)(21)(22)(23)(24)(25)(26)(27)(28)(29)(30). Esta ocorreu no hemitórax direito em seis (40%) casos e no lado esquerdo em 9 (60%).…”

Section: Malformação Congénita Das Vias Aéreas Pulmonares -Experiênciunclassified

“…These authors claimed that post-natal prognosis is conditioned by the severity of the initial or post-operative respiratory distress. Post-operative mortality has been documented in rare cases of bilateral CCAML 24,25 or associated to severe lung underdevelopment 26,27 . In conclusion, we can say that CCAML is a rare lung malformation which can cause respiratory distress in neonates.…”

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confidence: 99%

“…pós-operatória tem sido documentada em raros casos de MACPC bilateral 24,25 ou associada a severa hipoplasia pulmonar 26,27 . Em conclusão, podemos dizer que a MACPC é uma malformação pulmonar rara, que pode causar dificuldade respiratória no recém-nascido.…”

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Congenital cystic adenomatoid malformation of the lung – The experience of five medical centres

Rocha

Fernandes

Proença³

et al. 2007

Revista Portuguesa de Pneumologia (English Edition)

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ResumoIntrodução: O espectro clínico da malformação adenomatóide cística pulmonar congénita (MACPC) varia desde lesões assintomáticas e dificuldade respiratória no recém-nascido a hidrópsia fetal. Objectivos: Avaliação da casuística de MACPC, realçando a história natural, tratamento e evolução. Material e métodos: Análise retrospectiva dos processos clínicos de todos os recém-nascidos com o diagnóstico de MACPC, admitidos nas unidades de cui- Abstract Background:The clinical spectrum of congenital cystic adenomatoid malformation of the lung (CCAML) ranges from asymptomatic lesions to neonatal respiratory distress and hydrops fetalis. Aim: To review our experience with CCAML, emphasising natural history, management and outcome. Material and methods: A retrospective chart review of all CCAML-diagnosed neonates admitted

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Section: Malformação Congénita Das Vias Aéreas Pulmonares -Experiênciunclassified

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Congenital cystic adenomatoid malformation of the lung – The experience of five medical centres

Rocha

Fernandes

Proença³

et al. 2007

Revista Portuguesa de Pneumologia (English Edition)

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Bronchopulmonary‐foregut malformations:A continuum of paracrine hamartomas?

1997

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The bronchopulmonary-foregut malformations (BPFM) are usually sporadic, solitary cystic hamartomas involving conducting airways, arteries, venous drainage, and lung parenchyma. Transitional, compound hamartomas exist, and only their morphology is well-known. Between 1984-1994 we encountered and studied 10 unrelated patients and a stillborn infant with BPFM (out of 24,000 families). Ten were diagnosed in utero and one at birth as having congenital cystic adenomatoid malformation of the lung (CCAML). Postnatally, two diagnoses (20%) were corrected to bronchogenic cyst (BC) and diaphragmatic hernia, respectively. Bilateral lung involvement was present in 1 patient, and in 2 there was a considerable macroscopic regression of the hamartoma. Histologic studies of the six resected CCAML confirmed the diagnosis and implied dysregulated paracrine growth with its cellular and extracellular growth factors, protooncogenes, oncogenes, cytokines, cell-adhesive molecules, and receptors of these regulatory peptides, and their complex interactions as developmental morphogens in time and space.

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Bronchioloalveolar carcinoma arising in congenital cystic adenomatoid malformation in a child: A case report and review on malignancies originating in congenital cystic adenomatoid malformation

et al. 1998

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A type I congenital cystic adenomatoid malformation (CCAM) in the left lower lobe was removed from a 11‐year‐old boy with a 3‐month history of recurrent pneumonia. As incidental finding, a bronchioloalveolar carcinoma (BAC) was found in the lung parenchyma adjacent to the cyst. A left lower lobectomy was performed. At 18 months after surgery the patient is well and free of neoplastic disease. To the best of our knowledge, this association has not been reported previously in a pediatric patient. Malignancies complicating CCAM are rarely seen, but have been reported in adults. Including our case, eight cases of BAC and five cases of rhabdomyosarcoma (RMS) in association with CCAM have been reported so far. As CCAM can host metaplastic mucous cells, primitive mesenchymal cells and differentiated but poorly organized striated muscle fibers, it has been proposed that CCAM may act as a predisposing condition for oncogenesis. Our experience adds further support that CCAM can act as a premalignant lesion. Previous reports of both BAC and RMS in asymptomatic CCAM suggest prompt resection shortly after diagnosis. Pediatr. Pulmonol. 1998; 25:62–66. © 1998 Wiley‐Liss, Inc.

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Respiratory problems and cystic adenomatoid malformation of lung.

Cited by 20 publications

References 5 publications

Congenital cystic adenomatoid malformation of the lung – The experience of five medical centres

Congenital cystic adenomatoid malformation of the lung – The experience of five medical centres

Bronchopulmonary‐foregut malformations:A continuum of paracrine hamartomas?

Bronchioloalveolar carcinoma arising in congenital cystic adenomatoid malformation in a child: A case report and review on malignancies originating in congenital cystic adenomatoid malformation

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