Right atrial spindle cell sarcoma as a rare cause of tricuspid stenosis

Shewale, Sunil; Bhat, Prabhavathi; Gupta, Anshul; Manjunath, Cholenahally Nanjappa

doi:10.1136/bcr-2016-216373

Cited by 3 publications

(1 citation statement)

References 8 publications

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“…Several treatments have been reported for cardiac spindle cell sarcoma, but the effect is poor. Surgical resection with negative margins has been recommended as the gold standard of treatment so far [8]. Nevertheless, the mean survival of patients was 3 months to 1 year because of incomplete tumour resection and malignancy recurrence [2,9].…”

Section: Discussionmentioning

confidence: 99%

Spindle cell sarcoma of the right atrium causing right atrial pseudoaneurysm: a case report and review of the literature

Wang

Dong

Wei-jun

et al. 2021

J Cardiothorac Surg

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Background Spindle cell sarcomas of the right atrium are extremely rare primary cardiac tumours, with very few cases reported in the medical literature. Pseudoaneurysms caused by cardiac spindle cell sarcoma have never been reported worldwide. Case presentation A 32-year-old woman was referred to our hospital for recurrent pericardial haemorrhagic effusion and pleural effusion. Three-dimensional transthoracic echocardiogram, contrast chest CT, and contrast MRI revealed a pseudoaneurysm on the right side of the right atrium with a thrombus. There was a defect between the pseudoaneurysm and the right atrium. PET-CT suggested that FDG metabolism inhomogeneity increased in the mass in the right atrium. Exfoliative cytology detection of massive pericardial effusion and pleural effusion revealed no tumour cells. Spindle cell sarcoma of the right atrium was not confirmed until the patient underwent right thoracic exploration and biopsy. Before a confirmed diagnosis, symptomatic treatment, such as chest effusion and pericardium effusion drainage, and transfusion of red blood cells were mainly used to relieve the patient’s symptoms. Unfortunately, the patient was lost to optimal treatments and passed away 20 days after the pathological diagnosis was made. Conclusion The prognosis of spindle cell sarcomas remains poor due to delays in diagnosis, early metastasis and few available therapeutic options. Recurrent pericardial effusion and pleural effusion, especially in the nature of haemorrhagic effusion, and/or right atrial pseudoaneurysm shown on the transthoracic echocardiogram must be considered and highly suspected as malignancy by patients and physicians. If the diagnosis cannot be confirmed, histopathology should be performed as soon as possible to avoid losing the best treatment opportunity.

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Section: Discussionmentioning

confidence: 99%

Spindle cell sarcoma of the right atrium causing right atrial pseudoaneurysm: a case report and review of the literature

Wang

Dong

Wei-jun

et al. 2021

J Cardiothorac Surg

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Spindle cell sarcoma of the mitral valve: a rare indication for mitral valve replacement

Massey

Suvarna

Krawczyk

et al. 2017

European Journal of Cardio-Thoracic Surgery

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Right Atrial Intimal Sarcoma on 18F-FDG PET/CT

2020

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A right atrial mass was discovered with transthoracic cardiac ultrasound in a complaint-free, 81-year-old man at his yearly cardiological checkup. Further investigation of the mass with transesophageal cardiac ultrasound showed a well-defined nodular mass of approximately 3 × 3 cm, in close proximity to the posterior wall of the right atrium. The patient underwent an 18F-FDG PET/CT, which showed a right atrial mass with very high FDG uptake, suggesting a malignant process. The mass was surgically removed, and anatomopathological assessment revealed an intimal sarcoma, which is a very malignant tumor and an extremely rare occurrence at this location.

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Right atrial spindle cell sarcoma as a rare cause of tricuspid stenosis

Cited by 3 publications

References 8 publications

Spindle cell sarcoma of the right atrium causing right atrial pseudoaneurysm: a case report and review of the literature

Spindle cell sarcoma of the right atrium causing right atrial pseudoaneurysm: a case report and review of the literature

Spindle cell sarcoma of the mitral valve: a rare indication for mitral valve replacement

Right Atrial Intimal Sarcoma on 18F-FDG PET/CT

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