Scimitar Syndrome: About A Case Report and Review of the Literature

Abstract

Scimitar syndrome or Felson's veno-lobar syndrome is a very rare condition, characterised by the association of cardiopulmonary abnormalities namely an abnormal right pulmonary venous return which is most commonly located in the inferior vena cava. We present an observation of a seven-month-old female infant who presented with acute dyspnoea. The diagnosis was suspected on chest X-ray and confirmed on CT scan which showed a single large right pulmonary vein draining into the right atrium with a scimitar pattern in sagittal section associated with dextrocardia and pulmonary sequestration. The prognosis is related to the extent of the left-right shunt and associated malformations.