Scimitar Syndrome with Right Hemianomalous Pulmonary Venous Drainage into Superior Vena Cava/Right Atrium Junction

Kotecha, Monika Kantilal; Krishnamanohar, Soman R.; Kumar, Raghavannair Suresh

doi:10.1111/j.1747-0803.2011.00513.x

Cited by 5 publications

(2 citation statements)

References 11 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Cardiac catheterization and angiography confirm the diagnosis, giving detailed information about the patient's anatomy and the severity of the pulmonary hypertension. They are useful for surgical planning [11][12][13] .…”

Section: Discussionmentioning

confidence: 99%

Scimitar syndrome and anesthetic implications

Luna-Durán

González-Serrano

Echeverry

2015

Colombian Journal of Anesthesiology

View full text Add to dashboard Cite

IntubationChild Anesthesia a b s t r a c tWe present a clinical case report of a child with scimitar syndrome and a review of the literature in order to describe the main surgical and anesthetic implications of these patients. Child, 4 months old, weight 4700 g, diagnosed with pneumonia and left lobar emphysema requires mechanical intubation and ICU care. The associated diagnoses are failed extubation, severe pulmonary hypertension and scimitar syndrome confirmed with echocardiography. He was scheduled for pulmonary lobectomy. His mother signed an informed consent authorization for anesthesia and surgery. The child entered surgery, intravenous anesthetic induction was performed and a central venous catheter, an arterial line, urinary catheter and pre-and post-ductal pulse oximeters were inserted. He required vasopressor support with dopamine and transfusion of red blood cells. No adverse events during surgery. At the end of the surgery he was carried back to pediatric ICU and intubated with a chest tube. Extubation was successfully performed 2 days later with favorable progress. Scimitar syndrome is characterized by an anomalous right pulmonary venous return associated with congenital heart disease and pulmonary malformations. It has a low prevalence in the population but a very high perioperative morbidity and mortality, especially in children.With this report we present the main standards and practices for anesthetic management, monitoring and hemodynamic goals with these patients.Cimitarra se caracteriza por un drenaje venoso pulmonar anómalo derecho asociado a cardiopatías congénitas y malformaciones pulmonares. Tiene una prevalencia baja dentro de la población pero una morbimortalidad perioperatoria muy alta sobretodo en niños. Con este reporte se presentan unas pautas concretas y prácticas para el manejo anestésico, la monitorización y las metas hemodinámicas de estos pacientes.

show abstract

Section: Discussionmentioning

confidence: 99%

Scimitar syndrome and anesthetic implications

Luna-Durán

González-Serrano

Echeverry

2015

Colombian Journal of Anesthesiology

View full text Add to dashboard Cite

show abstract

“…2 Many terms have been used by a number of authors to describe those cases that, although a close cousin, lack all the elements of the complete scimitar syndrome. 1,[3][4][5][6][7][8][9][10][11][12] There is, however, no general agreement about an exact classification of these variants. In this study, we report our experience of scimitar syndrome variants since 1992.…”

Section: T He Scimitar Syndrome Is a Constellationmentioning

confidence: 99%