Selective spleen scintigraphy in the diagnosis of polysplenia syndrome

Abstract

This report describes a case of polysplenia syndrome diagnosed by selective spleen scintigraphy. This syndrome is rarely encountered in the elderly. It is characterized by multiple splenuncules with a number of associated congenital anomalies involving the cardiovascular system and the viscera. The differential diagnosis of these intra-abdominal masses can sometimes be difficult and can be confused with lymphadenopathy or metastases. Furthermore, biopsy of the splenuncules may be hazardous. The diagnosis of polysplenia can be established in most instances by (99)Tc(m) labelled heat-denatured red blood cell selective spleen scintigraphy without biopsy.

Polysplenia syndrome with preduodenal portal vein detected in adults

“…Studies also include descriptions of cases that involve a number of very small spleens, a multilobular spleen with tiny accessory spleen, and an undivided spleen [2,7] .…”

Heterotaxy Polysplenia Syndrome Causing Intermittent Vomiting Due to Malrotation of the Duodenum in an Adult

“…Heterotaxy is a rare condition in which the internal thoraco-abdominal organs and vascular structures show abnormal arrangement in the left-right axis of the body (1). As being the part of heterotaxy syndrome, polysplenia refers to presence multiple splenules without a parent spleen (2). The reported incidence of polysplenia is 1 per 250,000 live births (3).…”

Polysplenia Syndrome:A Rare Case Report with Computerized Tomography Findings

“…1 PS insidansı yaklaşık olarak 2.5:100.000 canlı doğum olarak rapor edilmiştir. 2 Tanı genellikle insidental olarak abdominal ultrasonografi (US) incelemesi sırasında konur. 3 Bu olgu bildirisinde abdominal, vasküler ve torasik anomalileri bulunan ve PS tanısı alan olgunun bilgisayarlı tomografi (BT) bulguları sunulmuştur.…”