Shrinking lung syndrome (SLS) associated with systemic lupus erythematosus (SLE): A series of cases in a university hospital

Casey, Alberto; Perin, Maria Marta; Enghelmayer, Juan Ignacio; Legarreta, Cora Gabriela; Zenón, Federico; Rossi, Pamela; Acuña, Silvana; Betancourt, Albio Ferrá; Gómez, Roberto; Beron, A.; Dubinsky, Diana; Putruele, Ana María

doi:10.1183/13993003.congress-2019.oa5329

Cited by 2 publications

(2 citation statements)

References 0 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Other interesting presentations focused on different diseases. C asey et al [ 79 ] showed a 4.4% prevalence of shrinking lung syndrome in an Argentinian cohort of systemic lupus erythematosus patients, with a median time to diagnosis of 30 months. In a Portuguese series of patients with organising pneumonia, azithromycin as second-line therapy led to resolution in 69% of cases, reinforcing the potential usefulness of macrolides in this disease [ 80 ].…”

Section: Rare Ilds/dpldsmentioning

confidence: 99%

ERS International Congress, Madrid, 2019: highlights from the Interstitial Lung Diseases Assembly

et al. 2020

View full text Add to dashboard Cite

This article discusses a selection of the scientific presentations in the field of interstitial lung diseases (ILDs) that took place at the 2019 European Respiratory Society International Congress in Madrid, Spain. There were sessions from all four groups within Assembly 12: group 12.01 “Idiopathic interstitial pneumonias”, group 12.02 “ILDs/diffuse parenchymal lung diseases (DPLDs) of known origin”, group 12.03 “Sarcoidosis and other granulomatous ILDs/DPLDs” and group 12.04 “Rare ILDs/DPLDs”. The presented studies brought cutting-edge developments on several aspects of these conditions, including pathogenesis, diagnosis and treatment. As many of the ILDs are individually rare, the sharing of experiences and new data that occur during the Congress are very important for physicians interested in ILDs and ILD patients alike.

show abstract

Section: Rare Ilds/dpldsmentioning

confidence: 99%

ERS International Congress, Madrid, 2019: highlights from the Interstitial Lung Diseases Assembly

et al. 2020

View full text Add to dashboard Cite

show abstract

“…SLS was considered in those with exertional dyspnea, restrictive pulmonary function tests (PFTs) and elevated copula of the diaphragm. Casey et al, (6) recorded 10 (4.44%) cases with SLS out of 225 SLE patients. It may complicate SLE at any time over its course, ranging from as early as 1 month to 35 years after disease onset.…”

Section: Introductionmentioning

confidence: 99%

Shrinking Lung Syndrome in Systemic Lupus Erythematosus

Osman,

Omar,

Elameen

et al. 2022

Minia Journal of Medical Research

View full text Add to dashboard Cite

Shrinking lung syndrome (SLS) is a rare complication of systemic lupus erythematosus (SLE), however it was also reported with other connective tissue diseases (CTDs). It is characterized by its low prevalence with higher incidence in females patients. Although it is much more frequent in advanced stages of the disease, rarely, SLS may be the presenting manifestation of SLE. It was found that it mostly occurs in patients without previous or concomitant major organ involvement, moreover in inactive stages of the disease. Progressive exertional dyspnea accompanied by pleuritic chest pain are considered the dominant symptoms in SLS. Pulmonary function tests (PFTs) with reduced lung volumes and radiographic finding of elevated diaphragmatic copula are the characteristic features in SLS. There are no standardized guidelines for the treatment of SLS in SLE. However, the majority of patients showed good response on medium to high doses of glucocorticoids. Moreover, an immunosuppressive agent should be added if the patient fails to improve on steroids alone.

show abstract

Shrinking lung syndrome (SLS) associated with systemic lupus erythematosus (SLE): A series of cases in a university hospital

Cited by 2 publications

References 0 publications

ERS International Congress, Madrid, 2019: highlights from the Interstitial Lung Diseases Assembly

ERS International Congress, Madrid, 2019: highlights from the Interstitial Lung Diseases Assembly

Shrinking Lung Syndrome in Systemic Lupus Erythematosus

Contact Info

Product

Resources

About