Shunts porto-systémiques congénitaux : expérience du Grand-Ouest sur cinq ans

Hubert, G.; Giniès, J.-L.; Dabadie, A.; Tourtelier, Y.; Willot, S.; Pariente, D.; Lefrançois, T.; Caldari, Dominique

doi:10.1016/j.arcped.2014.08.033

Cited by 8 publications

(14 citation statements)

References 13 publications

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“…Thus, data were obtained from 27 cases, 2,9,15,18 with 22 (82%) fetuses diagnosed with intra‐hepatic CPSS 2,9,15,18 and 5 (18%) with extra‐hepatic CPSS 17,18 . The use of different sub classification systems did not allow a more in‐depth analysis.…”

Section: Resultsmentioning

confidence: 99%

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Congenital intra‐hepatic porto‐systemic shunts diagnosed during intrauterine life: Systematic review

Carneiro

Rossi

Oliveira

et al. 2022

J of Clinical Ultrasound

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Objective: To describe the ultrasonographic characteristics of congenital portosystemic venous shunts (CPSS) diagnosed during pregnancy, their outcomes, and their evolution.Methods: Two independent researchers selected 493 review articles and case reports through the analysis of titles, abstracts, and full text. The PubMed and LILACS databases were searched. Through the application of filters according to the PRISMA protocol, only six articles were used in the research. The following information was collected, when available: gestational age at diagnosis, gender, birth weight, type of shunt, associated anomalies/complications and treatment/progression. Results:The data were obtained from 27 cases, with 22 (82%) fetuses diagnosed with intra-hepatic CPSS and 5 (18%) with extra-hepatic CPSS. The median time of intrauterine diagnosis was 33 weeks. In 12 (57.1%) of the 21 pregnancies evaluated, delivery was preterm. The estimated fetal weight ranged from 1150 to 3760 g, with 4 (25%) cases at <3rd, 3 (18.75%) cases at <10th, 8 (50%) cases at <50th, and 1 (6.25%) case at >97th percentile for gestational age. The most frequent obstetric complication was fetal growth restriction, which occurred in nine (60%) cases. As for postnatal treatment, 19 (70.4%) cases were conservatively treated, and 8 (29.6%) cases required surgical intervention. Conclusion:The diagnosis of CPSS still represents a challenge during prenatal care.Its early identification aims to provide guidance to pregnant women and their families, as well as follow-up and anticipation of possible complications, in addition to the evaluation of the mode of delivery and postnatal follow-up, directing the short-and long-term prognosis.

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Section: Resultsmentioning

confidence: 99%

“…The most frequent associated obstetric complication was fetal growth restriction (FGR), which occurred in 9 (60%) cases 2,16,17 . Associations, such as fetuses small or large for gestational age, cardiac malformations, changes in amniotic fluid volume, hyperechogenic bowel and placentomegaly, were also identified.…”

Section: Resultsmentioning

confidence: 99%

Congenital intra‐hepatic porto‐systemic shunts diagnosed during intrauterine life: Systematic review

Carneiro

Rossi

Oliveira

et al. 2022

J of Clinical Ultrasound

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“…These include enlargement of the umbilical vein and/or inferior vena cava, and the absence of an abnormally large ductus venosus is also an indirect sign of CPF. Postnatally and at any age, it can be discovered during an abdominal ultrasound for another indication; during an abnormal neonatal screening for galactosemia; high concentrations of galactose can be present in the plasma of newborns without an enzymatic deficiency of galactose metabolism [5]; during the etiological diagnosis of a complication; or during a workup for an associated malformation.…”

Section: Discussionmentioning

confidence: 99%

Congenital Portosystemic Hepatic Fistula: A case report

Elouardighi¹,

Zizi²,

Iaziji³

et al. 2023

World J. Bio. Pharm. Health Sci.

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Congenital portosystemic fistula (CPF) is a congenital malformation defined by one or more communications between a hepatic portal venous system and a systemic venous cava. Other terminologies exist in the literature, in particular for extrahepatic communications, such as "Abernethy malformation". It may be associated with other malformations or syndromes. Because of this non-physiological vascular communication, PFC can lead to the development of extrahepatic complications: hepatic encephalopathy and pulmonary vascular diseases (hepato-pulmonary syndrome or pulmonary hypertension). It can also lead to hepatic complications with the appearance of benign or malignant tumors and biological and metabolic disorders. We report the case of a newborn with a portosystemic hepatic fistula discovered during neonatal jaundice with cutaneous angiomatosis.

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“…However, if it does not close until the age of 2 years, intervention should be considered 68 - 10 , 13 Based on this knowledge, we opted for watchful waiting until our patient completed 2 years of age or until the appearance of signs of complications.…”

Section: Discussionmentioning

confidence: 99%

“…, 10 Pulmonary hypertension can be resolved, provided that the shunt is corrected before the development of irreversible vascular lesions 8. There is also improvement of cognitive function and recovery of weight and height in the presence of these changes 10…”

Section: Discussionmentioning

confidence: 99%

Shunt portossistêmico congênito intra‐hepático diagnosticado na vida intrauterina

Bellettini

Wagner

Balzanelo

et al. 2016

Revista Paulista de Pediatria

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Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.

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Shunts porto-systémiques congénitaux : expérience du Grand-Ouest sur cinq ans

Cited by 8 publications

References 13 publications

Congenital intra‐hepatic porto‐systemic shunts diagnosed during intrauterine life: Systematic review

Congenital intra‐hepatic porto‐systemic shunts diagnosed during intrauterine life: Systematic review

Congenital Portosystemic Hepatic Fistula: A case report

Shunt portossistêmico congênito intra‐hepático diagnosticado na vida intrauterina

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