Syndrome de Klippel-Trenaunay

Samimi, Mahtab; Lorette, G.

doi:10.1016/j.lpm.2009.10.016

Cited by 16 publications

(7 citation statements)

References 37 publications

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“…PWS is a complex vascular anomaly that manifests from birth itself [ 6 ]. It is considered a rare disorder, with an estimated incidence of one case per 100,000 individuals [ 7 ].…”

Section: Discussionmentioning

confidence: 99%

“…Superficial anomalies range from small vein ectasia to persistent embryonic veins and large venous malformations. Deep malformations encompass aneurysmal dilatation, aplasia, hypoplasia, duplications, and venous insufficiency [ 6 ]. It is noteworthy that upper limb involvement, as observed in our case, is relatively rare compared to lower limb manifestations [ 8 ].…”

Section: Discussionmentioning

confidence: 99%

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Pediatric Limb Asymmetry: A Unique Presentation of Angioosteohypertrophic Syndrome

Salhi,

N'joumi,

Banana

et al. 2024

Cureus

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Parks-Weber syndrome (PWS), also known as Klippel-Trenaunay-Weber syndrome, is a rare congenital bone vascular syndrome first described in 1900. It is characterized by arteriovenous malformations in a limb, leading to disproportionate limb growth and potential heart failure. Unlike Klippel-Trenaunay syndrome, PWS manifests arteriovenous malformations with abnormal connections between the arteries and veins of the affected limb. The management of this syndrome, similar to that of Klippel-Trenaunay syndrome, relies mainly on symptomatic treatment. We report the first case of angioosteohypertrophic syndrome diagnosed at CHU Med VI Oujda, in a patient aged seven years and eight months. This syndrome manifested primarily in the right upper limb, characterized by asymmetry in both upper limbs, thermal disparity, a cutaneous nevus, and venous ectasia in the right arm. The diagnosis was further substantiated through arteriography, confirming the presence of an arteriovenous fistula.

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“…PWS is a complex vascular anomaly that manifests from birth itself [ 6 ]. It is considered a rare disorder, with an estimated incidence of one case per 100,000 individuals [ 7 ].…”

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Pediatric Limb Asymmetry: A Unique Presentation of Angioosteohypertrophic Syndrome

Salhi,

N'joumi,

Banana

et al. 2024

Cureus

View full text Add to dashboard Cite

show abstract

“…Management is multidisciplinary and involves especially venous control and orthopedic management of unequal limb lengths. (11) May be associated with limb swelling , pain, gangrene ,venous ulcers, developmental defects include polydactyly, oligodactyly, macrocephaly, blue nevi, pulmonary vein varicosities, cerebral aneurysm, gastrointestinal hemorrhage, pulmonary embolism, incompetent valves in veins, and visceral venous malformations .…”

Section: Discussionmentioning

confidence: 99%

Klippel-Trenaunay Syndrome:A Rare Cause of NonHealing Ulcer

Mahawer¹,

Bothra²,

Gupta³

et al. 2014

IOSRJDMS

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“…Klippel-Trénaunay syndrome (KTS) is a congenital malformation with an incidence of 1 out of 27,500 live births described in 1900 including a triad of port-wine stain/capillary vascular malformation, venous malformation/varicose veins, soft tissue, and bony hypertrophy in affected limbs [ 1 ]. Although a combined spinal-epidural technique for an elective cesarean section and an epidural analgesia for vaginal delivery have been already presented [ 2 , 3 ], this is the first report that describes spinal anesthesia for an urgent cesarean section in a patient with KTS.…”

mentioning

confidence: 99%