“…A male predilection of 1.7:1-2:1 has been reported in three surgical series [12][13][14] . Considering its postulated autoimmune pathogenesis, it has been associated with Sjogren's syndrome [15,16] , rheumatoid arthritis [14] , primary sclerosing cholangitis [16,17] , retroperitoneal fibrosis [18] and inflammatory bowel disease [19] . Although the prevalence of a concurrent autoimmune diagnosis has been reported in various series, they are likely underestimates as some diagnoses of autoimmune pancreatitis may precede the diagnosis of the concurrent autoimmune condition [9,10,20] .…”