Tumor miofibroblástico de vejiga

Abstract

TUMOR MIOFIBROBLASTICO DE VEJIGA El tumor miofibroblásticos es un tumor mesenquimal benigno de carácter excepcional, siendo su localización mas habitual es el pulmón; mientras que su aparición en la vejiga, es excepcional, no existiendo mas de 100 casos publicados, de este tipo de tumor en la vejiga. Este tipo de tumor queclínica y radiológicamente, se comporta como un tumor maligno. El diagnóstico patológico es complejo, debido a su similitud con los sarcomas, siendo necesario recurrir a la inmunohistoquímica para un diagnostico de certeza.El tratamiento mediante resección amplia suele ser suficiente no existiendo en la actualidad ningún caso de metástasis a distancia, ni de malignizacion. Presentamos un nuevo caso de este tumor, realizando una amplia revisión bibliográfica.Palabras clave: Pseudotumor inflamatorio. Pseudosarcoma vesical. ABSTRACT MIOFIBROBLASTIC TUMOR OF BLADDERThe miofibroblastic tumor, is a mesenchimal benign tumor of exceptional character, being its localization but habitual it is the lung; while its appearance in the bladder, is exceptional, not existing but of 100 published cases, of this tumor type in the bladder. This tumor type that clinic and radiologics, behave as a wicked tumor. The pathological diagnosis is complex, due to its similarity with the sarcomas, being necessary to appeal to the inmunohistoquimics for a I diagnose of certainty.The treatment by means of wide resection is usually enough not existing any case of metastasis at the present time at distance, neither of malignization. We present a new case of this neoplasm, carrying out a wide bibliographical revision.

Inflammatory Myofibroblastic Bladder Tumor in a Patient with Wolf-Hirschhorn Syndrome

“…In our patient, there was no evidence of related infection or traumatic episode. IMT presents morphologic, immunophenotypic, endoscopic, and radiologic overlap with malignant spindle cells tumors of the urinary bladder, and differentiation from these tumors may be difficult [7]. Both epithelial and myogenic markers can be expressed in IMT and this coexpression may lead to a misdiagnosis of sarcomatoid carcinoma, leiomyosarcoma, and rhabdomyosarcoma [8–10].…”