Two-staged Baerveldt glaucoma implant for childhood glaucoma associated with Sturge-Weber syndrome31The authors have no proprietary interest in any of the materials used in this study.

A Multidisciplinary Consensus for Clinical Care and Research Needs for Sturge-Weber Syndrome

“…47,48 However, patients with SWS tend to have lower surgical success rates 49,50 and greater numbers of intra- and post-operative complications following glaucoma surgery. 51,52 As many as 60% of eyes treated with angle surgery require additional angle surgery and 40% require post-operative medications after 3–5 years. 53 Future randomized prospective studies would be helpful in determining a definitive treatment course, however are unlikely to be performed given the rare nature of the condition.…”

Retinal Detachment in a 40-Year-Old Man With Sturge-Weber Syndrome

“…Glaucoma in the patient’s right eye, likely owing to the latter, was refractive to medical therapy. He underwent 2-stage Baerveldt insertion—in the first stage, the plate was attached to the globe and 1 month later, allowing for scarring and capsule formation, the tube was placed into the anterior chamber . This approach has been reported effective at avoiding rapid intraocular pressure lowering that could result in fluid transudation due to increased hydrostatic pressure between the choroidal and abnormally high-pressure Sturge-Weber syndrome venous system .…”

Topical netarsudil for treatment of glaucoma with elevated episcleral venous pressure: A pilot investigation in sturge-weber syndrome

“…Due to the persistent IOP elevation above goal and progression of arcuate defects on HVF, inferonasal BGI implantation was performed via a two-staged approach. 11 At most recent follow-up of 26 months from netarsudil initiation (3 months after second stage of inferonasal BGI) IOP was reduced to 17 mmHg on netarsudil, latanoprost, timolol, brinzolamide-brimonidine. His BCVA was stable at 20/25 at last follow-up.…”