Uhl’s anomaly: a difficult prenatal diagnosis

Vaujois, Laurence; Doesburg, N. Van; Raboisson, Marie‐Josée

doi:10.1017/s1047951114000651

Cited by 4 publications

(2 citation statements)

References 9 publications

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“…Vaujois y cols. (11) describieron la cardiomegalia y el tabique interventricular desplazado hacia el ventrículo izquierdo con movimiento paradójico, como sugerentes de la anomalía, signos ecográficos que fueron también hallados en vida prenatal, sin embargo, concluyen que se trata de una patología de diagnóstico antenatal difícil.…”

Section: Discussionunclassified

Anomalía de Uhl: correlación de hallazgos ecográficos prenatales y posnatales

2022

revum

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La anomalía de Uhl es una cardiopatía congénita rara, caracterizada por la ausencia de miocardio en la pared del ventrículo derecho, la preservación de las trabeculaciones del septo interventricular derecho y la normalidad estructural de las válvulas tricúspide y pulmonar. Se ha planteado un probable origen congénito, pero no suele estar asociada con otras malformaciones cardíacas. La forma usual de presentarse es el fallo cardíaco congestivo, pero también se han observado arritmias y bloqueos cardiacos. La prevalencia general es de < 1/1 000 000. Se reporta un caso con hallazgos prenatales en paciente con un embarazo de 35 semanas, con cardiomegalia y dilatación ventricular derecha, correlacionados con hallazgos posnatales ecocardiográficos, con diagnóstico de anomalía Uhl. Se incluye imágenes ecocardiográficas pre-y posnatales con revisión bibliográfica.

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Section: Discussionunclassified

Anomalía de Uhl: correlación de hallazgos ecográficos prenatales y posnatales

2022

revum

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“…It should be differentiated from Uhl's anomaly, arrhythmogenic right ventricular dysplasia, and Ebstein anomaly. 6,7 Although causes of congenital VA have been described, its etiology is still mostly conjectures and hypotheses. 8,9 Saiki 9 showed that VA may be caused by placental vascular diseases that may lead to coronary embolism and stenosis.…”

Section: Discussionmentioning

confidence: 99%

Prenatal diagnosis of fetal right congenital ventricular aneurysms: An analysis of three cases and literature review

Zhong¹,

Song²,

Zhang³

et al. 2021

J of Clinical Ultrasound

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Right ventricular aneurysm is a rare congenital defect that can be diagnosed with fetal echocardiography. Information on etiology of right ventricular aneurysm is limited and its prognosis remains variable from asymptomatic forms to severe cases. Here we report three cases of fetal right ventricular aneurysms that could have been related to coronary artery disorders and needed regular monitoring of progression in size and signs of cardiac decompensation.

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Prenatal diagnosis of fetal right and left congenital ventricular aneurysms

Gowda

Bharathi

Thiagarajan

et al. 2017

The Journal of Maternal-Fetal & Neonatal Medicine

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Congenital ventricular aneurysm is a rare cardiac malformation characterized by protrusion or out pouching of a portion of the ventricular wall. It is important to differentiate an aneurysm from diverticulum, as the latter has favorable prognosis. The aneurysms are usually large and have broad-based communication with the ventricular cavity in contrast to diverticuli, which are small and connected by a narrow base.

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Uhl’s anomaly: a difficult prenatal diagnosis

Cited by 4 publications

References 9 publications

Anomalía de Uhl: correlación de hallazgos ecográficos prenatales y posnatales

Anomalía de Uhl: correlación de hallazgos ecográficos prenatales y posnatales

Prenatal diagnosis of fetal right congenital ventricular aneurysms: An analysis of three cases and literature review

Prenatal diagnosis of fetal right and left congenital ventricular aneurysms

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