Vaginal Aplasia with Functional Uterus: Two Cases and Review of Literature

Abstract

Maldevelopment of the vagina is usually combined with aplasia or hypoplasia of the uterus. Objective: To support the clinical peculiarities, imaging and surgical technique of this rare entity. Materials and Methods: This is a retrospective study conducted over 04 years. We collected two cases of vaginal aplasia with functional uterus. The diagnosis was based on clinical data, ultrasound, imaging. Results: Our patients had primary amenorrhea plus chronic, cyclic pelvic pain. The examination found partial vaginal aplasia for the first patient and complete vaginal aplasia for the second patient. Magnetic resonance imaging revealed atresia of the cervix with absence of the upper part of the vagina for the first case, an absence of the vagina for the second case. Both patients had vaginoplasty. The evolution was satisfactory for the first patient and the second evolution was marked by cervicovaginal stenosis, the patient had a hysterectomy. Conclusion: Whatever the surgical technique practiced, vaginoplasty allows in this rare malformation to restore the physical integrity and the sexual function, even if other case resulted in cessation to cervico-vaginal stenosis.