Rheumatic valvular disease in dextrocardia with situs inversus is said to be rare. Bleyer and Saphir (1953) have reviewed the literature on five hitherto published cases' and reported a sixth. According to them, Owen is credited with the first case report of mitral stenosis in dextrocardia with situs inversus, but since he could not definitely establish the aetiological factor for the mitral stenosis the authors did not include it in the review. Of the six cases reported, two were cases of aortic valvular affection, three of mitral stenosis with insufficiency, and one a case in which both mitral and aortic valves were involved.