A 22-year-old Australian woman with atypical subacute sclerosing panencephalitis diagnosed at postmortem

Fabian, V.; Lee, Hwei-Yee; Keith-Rokosh, Julia Lee; Souza, Jean-Louis de; Stewart-Wynne, E G

doi:10.1016/j.jocn.2009.12.016

Cited by 9 publications

(9 citation statements)

References 11 publications

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“…Another unusual feature of this patient was the rapid clinical course. About 10% of patients with SSPE follow an acute course, and acute cases are known to diverge from the classical clinical stages, and may lack both myoclonus and periodic EEG abnormalities, [12][13][14] similar to the present patient. Other atypical clinical presentations of SSPE include seizures and focal neurological deficits.…”

mentioning

confidence: 76%

Nocardia cyriacigeorgica abscess of the conus medullaris in an immunocompetent host

Lee¹,

Whitby²,

Hall³

2010

Journal of Clinical Neuroscience

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mentioning

confidence: 76%

Nocardia cyriacigeorgica abscess of the conus medullaris in an immunocompetent host

Lee¹,

Whitby²,

Hall³

2010

Journal of Clinical Neuroscience

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“…Generalized rigidity with extra-pyramidal features and unresponsiveness appear in stage 3. Stage 4 is the terminal stage of the disease and is characterized by minimal conscious state and later akinetic mutism associated with persistent high fevers and bouts of generalized sweating; both being due to autonomic failure3.The prognosis of SSPE is poor with death typically occurring within two to four years of onset as no curative treatment is available 3 . The diagnosis of SSPE is based on typical clinical features, periodic EEG complexes and elevated measles antibody titre in CSF.…”

Section: Discussionmentioning

confidence: 99%

An Unusual Findings of Elevated Urinary Copper Excretion in a Patient with Subacute Sclerosing Panencephalitis (SSPE): A Case Report

Islam

Chowdhury

Haq

et al. 2018

J. Natl Inst. Neurosci Bangladesh

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Subacute sclerosing panencephalitis is a progressive neurological disorder of childhood and early adolescence. It is caused by persistent defective measles virus1.We report a ten years old normally developed female patient who came with a history of drop attacks while walking, declining scholastic performance, progressively increasing myoclonic jerks. She had history of measles at five years of age though she was vaccinated as per EPI schedule. Physical examination and cerebrospinal fluid findings along with EEG changes in addition supported its diagnosis as a case of SSPE. The presence of increased urinary excretion of copper in SSPE is so far not yet reported in any published literature.Journal of National Institute of Neurosciences Bangladesh, 2017;3(2): 113-115

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“…SSPE remains an important public health issue in parts of the developing world due to limited measles immunization policies. 4 , 5 …”

Section: Discussionmentioning

confidence: 99%

Basal ganglia lesions in subacute sclerosing panencephalitis

Almeida

Brucki

Duarte³

et al. 2012

Dement. neuropsychol.

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The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.

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A 22-year-old Australian woman with atypical subacute sclerosing panencephalitis diagnosed at postmortem

Cited by 9 publications

References 11 publications

Nocardia cyriacigeorgica abscess of the conus medullaris in an immunocompetent host

Nocardia cyriacigeorgica abscess of the conus medullaris in an immunocompetent host

An Unusual Findings of Elevated Urinary Copper Excretion in a Patient with Subacute Sclerosing Panencephalitis (SSPE): A Case Report

Basal ganglia lesions in subacute sclerosing panencephalitis

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