A 72‐Year‐Old Man With Dyspnea, Circumferential Aortic Thickening, and Weight Loss

Erdheim–Chester disease: A systematic review

“…Based on the reported dramatic efficacy, it is conceivable that the use of Vemurafenib, up to date administered in only five patients [9,14,15], will increase in next years (Fig. 4).…”

New Insights in the Pathogenesis of Erdheim‐Chester Disease: Comment on the Article by Los Arcos‐Bertiz et al

“…We read with great interest the Clinicopathologic Conference by Los Arcos‐Bertiz et al published recently in Arthritis Care & Research about a patient with Erdheim‐Chester disease (ECD) who was treated effectively with interferon‐α (). Of note, the prognosis of this condition is poor, with 1‐ and 5‐year survival rates of 96% and 68%, respectively, because of resistant and progressive life‐threatening ECD, and interferon‐α can be responsible for a wide range of adverse events and potentially severe toxicities ().…”