A Case of Eczematid‐Like Purpura of Doucas and Kapetanakis in a Child

Abstract

Eczematid-like purpura of Doucas and Kapetanakis is a subtype of the pigmented purpuric dermatoses, a group of uncommon dermatoses of unclear etiology characterized by purpura, petechiae, and hyperpigmentation. The Doucas and Kapetanakis subtype is rare in children, and its subtle findings can initially be overlooked and mistaken for other, more common dermatologic disorders in this age group. We present a case eczematid-like purpura of Doucas and Kapetanakis in an 11-year-old boy initially treated as eczema.

The pathological spectrum and clinical correlation of pigmented purpuric dermatosis—A retrospective review of 107 cases

“…Pigmented purpuric dermatosis (PPD) comprises a group of skin diseases characterized by the presence of petechiae and/or purpura, particularly increased progressive pigmentation on the skin of lower extremities. PPD can be divided into several clinical subtypes according to clinical manifestations: non‐blanchable, red‐brown purpuric macules or pinhead sized puncta in Schamberg disease (progressive pigmentary dermatosis), polygonal to round lichenoid purpuric papules and plaques in pigmented purpuric lichenoid dermatosis of Gougerot and Blum (Gougerot‐Blum purpura), annular purpuric patches with telangiectasia in purpura annularis telangiectodes (Majocchi disease), gold‐brown lichenoid patches or plaques in lichen aureus, and eczematous purpuric macules and patches in eczematoid‐like purpura of Doucas and Kapetanakis (eczematoid‐like purpura) . PPD has also been associated with comorbid conditions .…”

“…However, the pathological features of PPD also range in duration and exhibit clinical variations. These differences can be as subtle as mild perivascular mononuclear cell inflammatory infiltrate, scant amount of erythrocyte extravasation and focal hemosiderin deposition in the papillary dermis, or can encompass dense lichenoid infiltration, spongiosis or granulomatous infiltration …”

Pigmented purpuric dermatosis in children: a retrospective cohort with emphasis on treatment and outcomes

“…The literature on paediatric PPD describes Schamberg disease as the most common subtype, with increasing reports of other PPD subtypes in children 6,7,38–40 . We found the highest prevalence to be the lichen aureus subtype, followed by Schamberg disease, the Majocchi subtype, and the Doucas and Kapetanakis subtype (Table 1).…”

Pigmented Purpuric Dermatosis of the Hand: Clinicopathologic Analysis of Six Cases With Review of the Literature

“…We identified 17 cases of PPD with hand involvement in the literature (Table 2). 8,11–21 Again, a wide age range was found (5–73 years; mean, 33 years). There was a male predominance (male-to-female ratio, 2.4:1).…”