A case of malignant carotid body tumor with metastases to the extradural space causing paraplegia is reported in a 29‐year‐old Jamaican woman. In only 2 of the 14 previously reported cases of carotid body tumor with distant metastases was there paraplegia, and both were due to tumor extension from vertebral bone metastases. It is suggested that the tumor in the present case reached the extradural space via direct venous communications with the neck.