A case of prune belly syndrome: Experience from a regional hospital in Togo

Essobiyou, Tamassi Bertrand; Kebalo, Sosso Piham; Pali, Essomondjona; Keheou, Alexandre Palissam; Issa, Mohamed; Dosseh, E.D.

doi:10.1016/j.ijscr.2022.107812

Cited by 1 publication

(2 citation statements)

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“…The disease affects males preferentially. 2 The incidence of PBS seems to be decreasing in developed countries because of prenatal diagnosis and the therapeutic interruption of pregnancy. 9 The etiology of PBS is currently uncertain, but there is some evidence of a possible family genetic inheritance.…”

Section: Discussionmentioning

confidence: 99%

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The challenging diagnosis and management of the prune belly syndrome: A case report

Kamoun,

Ben Hamed,

Abdenadher

et al. 2024

SAGE Open Medical Case Reports

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Prune belly syndrome is a rare disorder that occurs mainly in men. It is characterized by the triad of deficient abdominal wall muscles, the dilated urinary collecting system, bilateral cryptorchidism, and infertility. It mainly affects the genitourinary system, which involves the prognosis. We present the case of a preterm neonate male whose diagnosis of a prune belly was suspected in antenatal ultrasound. He had a urinary tract abnormality starting at 22 weeks of gestation. At birth, a clinical examination revealed a distended abdomen within a wrinkled and flaccid abdominal wall, a macropenis, and bilateral cryptorchidism. A urinary tract ultrasound revealed a right pyelocaliciel dilatation and a right megaureter with a megacystis. The neonate ultimately died due to severe renal failures. Prune Belly syndrome is a complex disease with a high mortality rate. Early antenatal ultrasound may ameliorate the prognosis.

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Section: Discussionmentioning

confidence: 99%

“… 1 It was first described by Frolish in 1839, with 95% of cases occurring in males and with male infertility. 2 It is characterized by abdominal flaccidity, urinary tract involvement, and cryptorchidism. The name “prune belly” refers to the wrinkled appearance of the abdomen, which is caused by a lack of muscle support.…”

Section: Introductionmentioning

confidence: 99%