A case of tracheal agenesis surviving without mechanical ventilation after external esophageal stenting

Watanabe, Takashi; Okuyama, Hiroomi; Kubota, Akio; Kawahara, Hiroyuki; Hasegawa, Toshimichi; Ueno, Takayoshi; Saka, Ryuta; Morishita, Yoshitaka

doi:10.1016/j.jpedsurg.2008.06.013

Cited by 32 publications

(22 citation statements)

References 13 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Forty-nine cases of TA, including our case, were found [1, 2, 4–7, 9–11, 14, 17, 18, 20, 23, 24, 26, 29–33, 35–38, 40, 42]. The perinatal characteristics, diagnostic investigations, and management are summarized (Table 1) .…”

Section: Resultsmentioning

confidence: 99%

“…Mortality was high, as 34 of 40 (85%) children died within 2 days. After surgery, two children are still alive at 10 months and 4 years, respectively [37, 40]. …”

Section: Resultsmentioning

confidence: 99%

“…Reconstruction with small intestine, colon interposition, or gastric pull-up has been demonstrated to be feasible and compatible with survival [24]. Despite progress in surgical management, only two children are still alive and have a normal neurodevelopment after surgery [37, 40]. …”

Section: Discussionmentioning

confidence: 99%

See 2 more Smart Citations

Tracheal agenesis: approach towards this severe diagnosis. Case report and review of the literature

et al. 2011

View full text Add to dashboard Cite

Tracheal agenesis (TA) is a severe congenital disorder with often an unexpected emergency presentation. There is complete or partial absence of the trachea below the larynx, with presence or absence of a tracheoesophageal fistula (TOF). A neonate with TA is described, and another 48 cases found in literature are reviewed. Due to absence of a TOF, five cases were diagnosed prenatally because of congenital high airway obstruction syndrome (CHAOS). When a TOF is present, polyhydramnion and several other congenital malformations seen on the ultrasound examination should alert clinicians of potential tracheal problems. Prenatal magnetic resonance imaging (MRI) may provide a definitive diagnosis. Postnatal diagnosis is based on recognition of specific clinical signs in the newborn with TA: respiratory distress with breathing movement without appropriate air entry, no audible cry, and failed endotracheal intubation. Despite progress in surgical interventions, mortality remains high. Prenatal diagnosis of TA is possible, but only if a TOF is absent resulting in CHAOS. Prenatal diagnosis of polyhydramnion and other congenital malformation should alert clinicians of potential tracheal problems. Prenatal MRI may provide a definitive diagnosis.

show abstract

Section: Resultsmentioning

confidence: 99%

“…Mortality was high, as 34 of 40 (85%) children died within 2 days. After surgery, two children are still alive at 10 months and 4 years, respectively [37, 40]. …”

Section: Resultsmentioning

confidence: 99%

See 1 more Smart Citation

Tracheal agenesis: approach towards this severe diagnosis. Case report and review of the literature

et al. 2011

View full text Add to dashboard Cite

show abstract

“…Other problems such as esophageal stenosis, ulceration, pneumonia, and aspiration after esophageal reconstruction may plague the child and result in an untimely demise [4]. No long-term data are available on recent attempts to use external esophageal stenting and donor aortas with a vascular stent [5]. Devising a "new" repair that would not require long-term reliance on positive pressure ventilation and would preserve the native esophagus seems warranted.…”

Section: To the Editormentioning

confidence: 99%

Brave new world or the unfortunate natural history of “lethal” disease: when to push the envelope?

Hartin¹,

Bass²,

Glick³

2011

Journal of Pediatric Surgery

View full text Add to dashboard Cite

“…Non-neoplastic tracheoesophageal fistulas can be congenital, (4,5) iatrogenic (6) or related to thoracic trauma. Once such a fistula has been diagnosed, surgical closure is formally indicated.…”

mentioning

confidence: 99%

Tratamento endoscópico de fístulas da árvore traqueobrônquica com dispositivos para a correção de defeitos do septo interatrial: resultados preliminares

et al. 2009

View full text Add to dashboard Cite

fistulas ranges from 0 to 28%, (1,2) and the mortality rate ranges from 16 to 72%. Non-neoplastic tracheoesophageal fistulas can be congenital, (4,5) iatrogenic (6) or related to thoracic trauma. Once such a fistula has been diagnosed, surgical closure is formally indicated. IntroductionFistulas in the tracheobronchial tree have a multifactorial etiology and present a variable incidence in the literature. The related morbidity and mortality are high. Bronchopleural fistulas usually result from surgical procedures involving pulmonary resection; the incidence of these Endoscopic treatment of tracheobronchial tree fistulas using atrial septal defect occluders: preliminary results* AbstractFistulas in the tracheobronchial tree (bronchopleural and tracheoesophageal fistulas) have a multifactorial etiology and present a variable incidence in the literature. In general, the related morbidity and mortality are high. Once such a fistula has been diagnosed, surgical closure is formally indicated. However, the clinical status of affected patients is usually unfavorable, which precludes the use of additional, extensive surgical interventions. In addition, attempts at endoscopic closure of these fistulas have seldom been successful, especially when the fistula is large in diameter. We report the cases of three patients submitted to endoscopic closure of fistulas, two of which were larger than 10 mm in diameter, by means of the insertion of atrial septal defect occluders. The procedure was minimally invasive, and the initial results were positive. The results indicate that this is a promising technique for the resolution of tracheobronchial tree fistulas.Keywords: Bronchial fistula; Tracheoesophageal fistula; Bronchoscopy; Respiratory therapy. ResumoAs fístulas da árvore traqueobrônquica, sejam elas broncopleurais ou traqueoesofágicas, apresentam etiologia multifatorial, com incidência variável na literatura. Em geral, apresentam alta morbidade e mortalidade, com indicação formal de correção cirúrgica. Entretanto, a condição clínica dos pacientes muitas vezes não permite uma reintervenção cirúrgica de grande porte. Além disso, as tentativas de fechamento endoscópico raramente têm sucesso, principalmente em fístulas de grande diâmetro. Relatamos os casos de três pacientes submetidos ao fechamento endoscópico de fístulas, sendo duas maiores que 10 mm, com a aplicação de dispositivos oclusores utilizados na cardiologia intervencionista, de forma minimamente invasiva e com resultados iniciais positivos. Esses dados sinalizam que essa pode ser uma técnica promissora na resolução de fístulas da árvore traqueobrônquica.

show abstract

A case of tracheal agenesis surviving without mechanical ventilation after external esophageal stenting

Cited by 32 publications

References 13 publications

Tracheal agenesis: approach towards this severe diagnosis. Case report and review of the literature

Tracheal agenesis: approach towards this severe diagnosis. Case report and review of the literature

Brave new world or the unfortunate natural history of “lethal” disease: when to push the envelope?

Tratamento endoscópico de fístulas da árvore traqueobrônquica com dispositivos para a correção de defeitos do septo interatrial: resultados preliminares

Contact Info

Product

Resources

About