A case report of Charcot arthropathy caused by syringomyelia and Chiari malformation complicated with scoliosis

Abstract

BackgroundAlthough Charcot arthropathy, also known as neuropathic arthropathy, of which early diagnosis and treatment is extremely difficult, associated with other cause factor has been widely described, Charcot arthropathy caused by syringomyelia and Chiari malformation complicated with scoliosis has never been described in the literature.Case presentationA 44-year-old male was hospitalized for diagnosis and treatment due to complaining the progressively swelling and limitation of motion in his left shoulder joint for 1 year. The patient has no significant past medical history except for scoliosis 8 years prior to his presentation to our clinic; He denied any constitutional symptoms, trauma, or pain in the upper extremities at this time of presentation. Based on history, physical and auxiliary examination, following diagnoses were made: Charcot arthropathy of the left shoulder, syringomyelia, Chiari malformation and scoliosis.ConclusionOnce Charcot arthritis was found, it was mostly in advanced stage and very difficult to treat. So we recommended that if patient suffering from scoliosis visited in clinic, further examination such as magnetic resonance imaging (MRI) and regular follow-up should be carried out, and early-stage of this devastating disease caused by syringomyelia and Chiari malformation may be diagnosed easily.

Neuroartropatia de Charcot secundária à siringomielia com acometimento isolado de ombro: relato de caso

“…(13). A patogênese da malformação de Chiari associada à siringomielia ainda é um assunto de muito debate na literatura (14). No caso apresentado, não houve associação com a malformação tipo I de Arnold-Chiari.…”

Syringomyelia with Chiari I Malformation Presenting as Hip Charcot Arthropathy: A Case Report and Literature Review

“…Other rare manifestations of syringomyelia include scoliosis [ 21 , 22 ], painless ulcers of the hands, edema, and hyperhidrosis, due to the interruption of central autonomic pathways [ 23 ].…”

The clinical efficacy study of treatment to Chiari malformation type I with syringomyelia under the minimally invasive surgery of resection of Submeningeal cerebellar Tonsillar Herniation and reconstruction of Cisterna magna

“…Spastic paralysis can be below the plane of the lesion, occurring the increasing muscle tension and negative abdominal wall and positive Babinski, which has higher disability rates. What’s more, it can also occur the dysfunction of the respiratory muscles, affecting the quality of patients seriously (Killeen et al, 2016, Liu et al, 2014). The database of syringomyelia shows about 75% patients suffer from this disease because of the Chiari malformation, and the type I, caused by heredity generally, is most common.…”