Arhinia is a congenital nasal developmental anomaly that is seldom reported in literature, and especially not reported in domestic animals. This report describes a case of concurrent occurrence of congenital arhinia and choanal atresia in a day-old male kid which had no external nares with the nasal bones fused together with the nasal processes of the premaxillae presententing as a conical shaped rhinal structure with a tapering rostral apex and an occluded nasal vestibule. A bilateral osseous choanal atresia was also seen at the pharynx. Additionally, craniofacial and brain anomalies presented in this condition with right lateral deviation of the face and the absence of olfactory apparatus including olfactory bulbs, tracts and nerves and a vestigial trigonum olfactorium were noted. This, to the best of our knowledge is the first report in the literature indexed in the Medline of concurrent occurrence of congenital arhinia and choanal atresia in a goat.