A Cautionary Tale of Vascular Abnormalities in Klippel-Trenaunay Syndrome: A Case Report

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterized by a port-wine stain birthmark, venous anomalies, and soft-tissue hypertrophy. Diagnosis of KTS is made based on two of the three characteristic diagnostic features. Klippel-Trenaunay syndrome is unilateral and more commonly affects the lower extremities. This case report describes a unique patient who lacked a patent deep system in the affected limb, making the traditional treatment of varicosities a dangerous outcome for this patient.