A clinicopathological study of Dermatofibrosarcoma Protuberans in Maiduguri, Northeastern Nigeria

Abstract

Background Dermatofibrosarcoma protuberans (dfsp) is a rare tumour originating from the dermis, it is slow growing, nodular, polypoid neoplasm that invade the subcutaneous tissue and does not usually metastasis.Clinical presentation is not uniform and may mimic common tropical benign skin lesions.We intend to study the behaviour of this tumour in our environment . Materails and method. A Clinicopathologic study of 36 cases of histologically diagnosed Dermatofibrosarcoma protuberans in University Maiduguri Teaching Hospital was carried out.DFSP constitutes 3.05% of all cases of all cancers and 10.2 % of all skin cancers. The peak age incidence was the 4 th and 6 th decades with a median age 37.6 years. The males to female ratio was 2:1. The commonest site was the trunk 17(48.8%), followed by the lower limbs 8 (22.9%); upper limbs 6(17.1%); head and neck 3(8.6%) and buttock 1(2.9%) were not frequently affected.. Conclsusion: DFSP is a common lesion in our environment that warrants proper clinical assessment, and histological characterisation.

Dermatofibrosarcoma Protuberans of the Breast—a Rare Entity

“…Large lesions often are associated with satellite nodules. Immunohistochemistry is an important tool for diagnosis [1,6]. Most of them are CD4 positive.…”

Dermatofibrosarcoma Protuberance of the Breast: a Diagnostic Challenge

“…It is known to be locally aggressive, though metastases are rare and when occur affect the lungs and the lymph nodes [2] .It usually presents in the middle age between the fourth to sixth decade but can occur at all ages [2][3][4]. Its presentation varies from an asymptomatic skin-coloured plaque, to a nodular lesion which may sometime ulcerate [2].…”