A late presentation of scimitar syndrome in adult

Abstract

Scimitar Syndrome is a rare congenital disorder and a variant of partial anomalous pulmonary venous connection (PAPVC) in which part or even the entire right lung is drained by right pulmonary veins that connect anomalously to the Inferior Vena Cava (IVC). It has various presentations including exertional dyspnea, recurrent chest infection, pulmonary artery hypertension, and hemoptysis. The initial diagnosis of PAPVC may be made by echocardiography and is typically confirmed by magnetic resonance imaging, computed tomography, or cardiac catheterization.We report a 69-year-old man with progressive dyspnea on exertion associated with palpitations of five years of evolution. The patient was diagnosed with cardiomyopathy, pulmonary hypertension and was started on treatment with anticoagulation, digoxin, and metoprolol for his atrial fibrillation. Despite the treatment, the dyspnea did not improve. The patient underwent cardiac catheterization, where the anomalous venous drainage was confirmed. Scimitar syndrome was corrected by surgical intervention with complete resolution of symptoms.

An 8‐year‐old boy with Scimitar syndrome: Presentation with gastroesophageal reflux symptoms and concurrent associations, including ectopic herniated liver

“…4 Another recent case report identified a SS diagnosis in a 69-year-old man with gastroesophageal reflux disease, along with findings of arterial hypertension, atrial fibrillation, hypothyroidism, and palpitations. 5 Barium swallow esophagography should be conducted for patients diagnosed with SS who report gastroesophageal reflux symptoms. Additionally, it should be kept in mind that SS may present with reflux symptoms, although it is very rare.…”