“…Some authorities regard NBIE as a severe variant of LI, whereas others refer to it as “erythrodermic lamellar ichthyosis.” 1 Clinically, the differentiation of NBIE from other congenital dermatoses, such as congenital psoriasis, congenital pityriasis rubra pilaris, and Leiner's disease, is sometimes difficult 1 . NBIE is inherited as an autosomal‐recessive trait 1,7 . It may be caused by the same genetic entity as that which produces LI, with different clinical expression, 1,7 , 8 or by a different genetic entity 1,7 , 8 …”